Congenital absence of the portal vein in a boy

被引:46
|
作者
Kohda, E
Saeki, M
Nakano, M
Masaki, H
Ogawa, K
Nirasawa, M
Hiramatsu, K
机构
[1] Keio Univ, Sch Med, Dept Radiol, Shinjuku Ku, Tokyo 1608582, Japan
[2] Natl Childrens Hosp, Dept Radiol & Surg, Tokyo 154, Japan
[3] Nihon Kohkan Hosp, Dept Radiol & Paediat, Kawasaki, Kanagawa, Japan
关键词
D O I
10.1007/s002470050580
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Congenital absence of the portal vein (CAPV) is a malformation that is generally thought to be limited to females. We encountered an Ii-year-old boy with this malformation. In 17 previously reported cases of CAPV, 2 were male. Three male patients, including our case, were Abernethy type Ib malformation. They had no associated liver tumour and two had no additional congenital abnormality. Conversely, 13 of the 15 female patients had congenital abnormalities acid 6 had liver mass lesions.
引用
收藏
页码:235 / 237
页数:3
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