Necrotizing toxoplasmic encephalitis in a child with the X-linked hyper-IgM syndrome

被引:0
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作者
I. Tsuge
H. Matsuoka
A. Nakagawa
Y. Kamachi
K. Aso
T. Negoro
M. Ito
S. Torii
K. Watanabe
机构
[1] Department of Paediatrics,
[2] Nagoya University School of Medicine,undefined
[3] Tsurumai-cho 65,undefined
[4] Showa-ku,undefined
[5] Nagoya 466,undefined
[6] Japan,undefined
[7] Tel.: +8152-741-2111,undefined
[8] Fax: +8152-731-6137,undefined
[9] Department of Pathology,undefined
[10] Nagoya University Hospital,undefined
[11] Nagoya 466,undefined
[12] Japan,undefined
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关键词
Key words Hyper-IgM syndrome; CD40 ligand; Necrotizing toxoplasmic encephalitis;
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摘要
We report on a 9-year-old boy with the hyper-IgM syndrome who presented with rapid impairment of consciousness. The brain CT scan showed multiple round lucencies, and the brain histology revealed necrotizing toxoplasmic encephalitis. This patient, whose CD40/CD40 ligand system was impaired, indicates the importance of this system for defence against toxoplasmic infection.
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页码:735 / 737
页数:2
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