Metastasized pancreatic neuroendocrine tumor in a teenage girl: a case report

被引:5
|
作者
Tremmel T. [1 ]
Holland-Cunz S. [2 ]
Günther P. [1 ]
机构
[1] Department of Pediatric Surgery, University Hospital Heidelberg, INF 110, Heidelberg
[2] Department of Pediatric Surgery, University Hospital Basel, Spitalstrasse 33, Basel
关键词
Functioning pancreatic neuroendocrine tumor (F-PanNET); Islet cell tumors; Non-functioning pancreatic neuroendocrine tumor (NF-PanNET); Pancreatic neuroendocrine tumor (PanNET); Yttrium-90 DOTATOC therapy;
D O I
10.1186/s13256-015-0708-3
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学科分类号
摘要
Introduction: Metastasized pancreatic neuroendocrine tumors are extremely rare malignancies, especially in children. Therefore, therapeutic options are limited, and few standardized therapy regimens exist. Case presentation: We report a case of a 14-year-old white girl. In 2011 she was diagnosed with a metastasized, well-differentiated pancreatic neuroendocrine tumor with expression of synaptophysin and chromogranin A. We describe her clinical course with special attention to her individual therapeutic regimens while bringing together several disciplines of medicine. Conclusions: In patients such as ours, surgical intervention may be the only therapy that will lead to long-term survival. © 2015 Tremmel et al.
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