Nager syndrome [Das Nager-Syndrom.]

被引：3
|
作者：
Opitz C. [1 ]
Shetty D.K. [1 ]
Witkowski R. [1 ]
机构：
[1] Zentrum für Zahnmedizin, Abteilung für Kieferorthopädie und Orthodontie, Universitätsklinikum Charité, Medizinische Fakultät, Humboldt-Universität Berlin.
来源：
Mund-, Kiefer- und Gesichtschirurgie | 1998年 / 2卷 / 3期
关键词：
Nager-Syndrom; Velumspalte; Genetische Prädisposition; Nager syndrome; Cleft velum; Genetic predisposition;
D O I：
10.1007/s100060050045
中图分类号：
学科分类号：
摘要：
In this publication, Nager syndrome was analyzed in the literature and six patients from our clinic were evaluated in relation to symptoms, etiology and pathogenesis. The diseases to be considered when making a differential diagnosis are pointed out. Clarification of the etiology is still pending. Molecular genetic research in these patients is possibly the key for new findings. A case report illustrates the results of interdisciplinary treatment by the surgeon and orthodontist. Possibilities and problems in relation to therapy are demonstrated.
引用
收藏
页码：122 / 126
页数：4
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