Tetralogy of Fallot with absent pulmonary valve in an adult

被引:0
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作者
Santhosh Regini Benjamin
Roy Thankachen
Sameer Mallampatti
Korah Thomas Kuruvila
机构
[1] The Christian Medical College (CMC Hospital),The Department of Cardiothoracic Surgery
关键词
Tetralogy of fallot; Absent pulmonary valve; Prosthetic valve; Bronchial compression;
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摘要
Absent pulmonary valve syndrome (APVS) is seen in around 3 to 6% of tetralogy of Fallot (TOF) patients. They present in the neonatal or infantile period with respiratory compromise, cardiac failure, or cyanosis. They rarely survive into adulthood with only few reports published in literature so far. In this report, we present an adult patient with TOF and APVS, who underwent a successful repair with prosthetic valve implantation.
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页码:198 / 200
页数:2
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