Dilated Cardiomyopathy in Epidermolysis Bullosa

被引:9
|
作者
Lara-Corrales, Irene [1 ]
Pope, Elena [1 ]
机构
[1] Hosp Sick Children, Toronto, ON M5G 1X8, Canada
关键词
Dilated cardiomyopathy; Epidermolysis bullosa; Carnitine; Selenium; CARDIAC AUTOANTIBODIES; CLINICAL-SIGNIFICANCE; SELENIUM DEFICIENCY; BETA-THALASSEMIA; CHILDREN; MYOCARDITIS; COLLAGEN; DEFECTS;
D O I
10.1016/j.det.2010.02.002
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Dilated cardiomyopathy (DC) is a rare but potentially fatal complication of epidermolysis bullosa. No clear cause for it has been identified, but iron overload, low carnitine, low selenium, concomitant viral illness, chronic anemia, and medications have been proposed as possible contributors to the development of DC in reported cases. Early detection allows for medical treatment that delays clinical progression and prolongs survival.
引用
收藏
页码:347 / +
页数:6
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