Idiopathic Pulmonary Arterial Hypertension in Childhood

被引：4
|
作者：
Haworth, Sheila G. [1 ]
机构：
[1] Great Ormond St Hosp Sick Children, Univ Coll Inst Child Hlth, London, England
来源：
CARDIOLOGY IN REVIEW | 2010年 / 18卷 / 02期
关键词：
idiopathic pulmonary arterial hypertension; pulmonary vascular disease; quality of life; prostacyclin; endothelin receptor antagonists; phosphodiesterase inhibitors; CHILDREN; SURVIVAL; BOSENTAN; THERAPY; EXPRESSION;
D O I：
10.1097/CRD.0b013e3181ce03df
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
The introduction of new medicines to treat pulmonary vascular disease has renewed interest in the management of children with idiopathic pulmonary arterial hypertension. We now have a practical classification of pulmonary hypertension, improved diagnostic techniques, and internationally recognized diagnostic and management guidelines. In 2009 the UK Pulmonary Hypertension Service for Children reported survival figures for idiopathic pulmonary arterial hypertension of 85.6% at 1 year, 79.9% at 3 years, and 71.9% at 5 years. A good quality of life can be assured for many years
引用
收藏
页码：64 / 66
页数：3
相关论文
共 50 条
  • [21] Survival In Rheumatoid Arthritis Associated Pulmonary Arterial Hypertension Is Comparable To Idiopathic Pulmonary Arterial Hypertension
    Sadeghi, S.
    Granton, J. T.
    Akhavan, P. S.
    Johnson, S. R.
    [J]. AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2013, 187
  • [22] Idiopathic pulmonary arterial hypertension misdiagnosed as asthma
    Hayes, Don, Jr.
    [J]. JOURNAL OF ASTHMA, 2007, 44 (01) : 19 - 22
  • [23] ARTERIAL PULMONARY-HYPERTENSION - SECONDARY OR IDIOPATHIC
    MUNDT, G
    GAGLIARDI, LM
    MARCARIAN, J
    SEMENIUK, G
    RONCORONI, A
    AGREST, A
    BASTAROLI, J
    GONZALEZSEGURA, R
    BOFFI, A
    [J]. MEDICINA-BUENOS AIRES, 1979, 39 (01) : 101 - 114
  • [24] Prednisolone Ameliorates Idiopathic Pulmonary Arterial Hypertension
    Ogawa, Aiko
    Nakamura, Kazufumi
    Mizoguchi, Hiroki
    Fujii, Nobuharu
    Fujio, Hideki
    Kusano, Kengo F.
    Ohe, Tohru
    Ito, Hiroshi
    [J]. AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2011, 183 (01) : 139 - 140
  • [25] Transplantation in children with idiopathic pulmonary arterial hypertension
    Lammers, A. E.
    Burch, M.
    Haworth, S. G.
    Elliott, M. J.
    Aurora, P.
    [J]. JOURNAL OF HEART AND LUNG TRANSPLANTATION, 2007, 26 (02): : S246 - S246
  • [26] Neovascularity in Patients with Idiopathic Pulmonary Arterial Hypertension
    Tuppin, M. P.
    Chambers, D.
    Slaughter, R.
    Mohammed, O.
    Kermeen, F.
    [J]. JOURNAL OF HEART AND LUNG TRANSPLANTATION, 2012, 31 (04): : S283 - S284
  • [27] Treprostinil lontophoresis in Idiopathic Pulmonary Arterial Hypertension
    Tonelli, Adriano R.
    Ahmed, Mostafa K.
    Alkukhun, Laith
    Cikach, Frank
    Aulak, Kulwant
    Dweik, Raed A.
    [J]. AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2015, 192 (08) : 1014 - 1016
  • [28] Treatment of idiopathic/hereditary pulmonary arterial hypertension
    Matsubara, Hiromi
    Ogawa, Aiko
    [J]. JOURNAL OF CARDIOLOGY, 2014, 64 (3-4) : 243 - 249
  • [29] A CASE OF IDIOPATHIC PULMONARY ARTERIAL HYPERTENSION IN MALE
    Paranthaman, Poongavanam
    Manian, Ramani Bala Subra
    Balaji, Thenrajan
    Jayakumar, Jayakrishnan
    Ranjani, Govindaraj
    [J]. JOURNAL OF EVOLUTION OF MEDICAL AND DENTAL SCIENCES-JEMDS, 2016, 5 (63): : 4494 - 4496
  • [30] Transplantation in children with idiopathic pulmonary arterial hypertension
    Lammers, A. E.
    Burch, M.
    Haworth, S. G.
    Elliott, M. J.
    Aurora, P.
    [J]. CLINICAL RESEARCH IN CARDIOLOGY, 2007, 96 (09) : 684 - 684
12345