A case of a 10-year old boy with an anterior spinal epidural hematoma in the cervical spine is presented. Subsequent to the MR examination clinical and laboratory work-up revealed the child to have a severe form of Hemophilia-A. Thee intraspinal bleeding was the first manifestation of this disease in the boy; the site of bleeding too was unusual. Subsequent imaging studies after treatment with Factor VIII replacement are also depicted. The pivotal role of MRI in the diagnosis of the hematoma is stressed. In a young male child with these clinical and imaging features, one should investigate the possibility of hemophilia and congenital coagulation defects.
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Univ Hlth Sci, Ankara Child Hlth & Dis Hematol Oncol Training &, Ankara, TurkeyUniv Hlth Sci, Ankara Child Hlth & Dis Hematol Oncol Training &, Ankara, Turkey
Bilir, Ozlem Arman
Yarali, Nese
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Univ Hlth Sci, Ankara Child Hlth & Dis Hematol Oncol Training &, Ankara, TurkeyUniv Hlth Sci, Ankara Child Hlth & Dis Hematol Oncol Training &, Ankara, Turkey
Yarali, Nese
Kacar, Dilek
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Univ Hlth Sci, Ankara Child Hlth & Dis Hematol Oncol Training &, Ankara, TurkeyUniv Hlth Sci, Ankara Child Hlth & Dis Hematol Oncol Training &, Ankara, Turkey
Kacar, Dilek
Kara, Abdurrahman
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Univ Hlth Sci, Ankara Child Hlth & Dis Hematol Oncol Training &, Ankara, TurkeyUniv Hlth Sci, Ankara Child Hlth & Dis Hematol Oncol Training &, Ankara, Turkey
Kara, Abdurrahman
Culha, Vildan
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Univ Hlth Sci, Ankara Child Hlth & Dis Hematol Oncol Training &, Ankara, TurkeyUniv Hlth Sci, Ankara Child Hlth & Dis Hematol Oncol Training &, Ankara, Turkey
Culha, Vildan
Ozbek, Namik Yasar
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Univ Hlth Sci, Ankara Child Hlth & Dis Hematol Oncol Training &, Ankara, TurkeyUniv Hlth Sci, Ankara Child Hlth & Dis Hematol Oncol Training &, Ankara, Turkey
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Seoul Sacred Heart Gen Hosp, Dept Orthoped, 259 Wangsan Ro, Seoul 130867, South KoreaSeoul Sacred Heart Gen Hosp, Dept Orthoped, 259 Wangsan Ro, Seoul 130867, South Korea
Ahn, Dong Ki
Jung, Woo Shik
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Seoul Sacred Heart Gen Hosp, Dept Orthoped, 259 Wangsan Ro, Seoul 130867, South KoreaSeoul Sacred Heart Gen Hosp, Dept Orthoped, 259 Wangsan Ro, Seoul 130867, South Korea
Jung, Woo Shik
Lee, Jae Il
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Seoul Sacred Heart Gen Hosp, Dept Orthoped, 259 Wangsan Ro, Seoul 130867, South KoreaSeoul Sacred Heart Gen Hosp, Dept Orthoped, 259 Wangsan Ro, Seoul 130867, South Korea