Familial Mediterranean fever and membranous glomerulonephritis: report of a case

被引:4
|
作者
Ceri, Mevlut [2 ]
Unverdi, Selman [2 ]
Altay, Mustafa [1 ]
Unverdi, Hatice [3 ]
Ensari, Arzu [3 ]
Duranay, Murat [2 ]
机构
[1] Ankara Educ & Res Hosp, Dept Internal Med, Ankara, Turkey
[2] Ankara Educ & Res Hosp, Dept Nephrol, Ankara, Turkey
[3] Ankara Univ, Fac Med, Dept Pathol, TR-06100 Ankara, Turkey
关键词
THE-LITERATURE; AMYLOIDOSIS; NEPHROPATHY; MUTATION; CHILDREN;
D O I
10.3109/08860221003640090
中图分类号
R5 [内科学]; R69 [泌尿科学(泌尿生殖系疾病)];
学科分类号
1002 ; 100201 ;
摘要
Familial Mediterranean fever (FMF) is an autosomal recessive genetic disease characterized by recurrent attacks of fever and painful episodes of sterile polyserositis. Kidney involvement may occur as a result of secondary amyloidosis during the course of FMF. Previously, different types of glomerulopathies such as IgM and IgA nephropathy, crescentic glomerulonephritis, diffuse proliferative glomerulonephritis, minimal change disease, and membranoproliferative glomerulonephritis were rarely reported. We herein represent a first case of membranous glomerulonephritis who had complete remission with colchicine treatment in the course of familial Mediterranean fever.</.
引用
收藏
页码:401 / 403
页数:3
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