An unusual case of primary systemic amyloidosis

被引:0
|
作者
Ambrosone, L
Mansi, L
Salvatore, T
Marino, F
Orabona, P
Rambaldi, A
Rambaldi, PF
Rambaldi, M
机构
[1] Univ Naples 2, Sch Med & Surg, Dept Dermatol, Ist Clin Med Reumatol, I-80131 Naples, Italy
[2] Univ Naples 2, Ist Sci Radiol Med Nucl, Naples, Italy
[3] Univ Naples 2, Ist Med Interna & Malattie Metab, Naples, Italy
[4] Univ Naples 2, Ist Clin Dermosifilopat, Naples, Italy
[5] Univ Naples Federico II, Ist Anat Patol, Naples, Italy
关键词
amyloidosis; external auditory canals; scintigraphy with technetium-99m (V) dimercaptosuccinic acid ([Tc-99m (V)] DMSA); therapy;
D O I
10.1016/S0926-9959(97)00086-X
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Here we report an unusual case of primary systemic amyloidosis, The cutaneous lesions were polymorphic and included involvement of both external auditory canals, The visceral involvement was covert. Mapping of amyloid deposits was performed using scintigraphy with technetium-99m (V) dimercaptosuccinic acid ([Tc-99m (V)] DMSA). Therapy with melphalan,prednisone and colchicine resulted in considerable improvement. (C) 1998 Elsevier Science B.V.
引用
收藏
页码:53 / 57
页数:5
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