A 68-year-old woman was admitted to our hospital with fever and pleural effusion. Her thoracentesis showed eosinophilic pleural effusion (EPE) without any evidence of malignancy, infection, or trauma. Pleural biopsy revealed pleuritis and intercostal myositis. Characteristic skin manifestations, including Gottron's sign, interstitial lung disease, and pericardial effusion, appeared later in the clinical course. She was finally diagnosed with anti-PL-7 antisynthetase syndrome (ASS) based on the presence of anti-PL-7 antibody, and she fulfilled the diagnostic criteria for dermatomyositis. These clinical manifestations improved with immunosuppressive therapy. EPE might therefore be one of the characteristic features of anti-PL-7 ASS.
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Univ Paris 05, Hop Cochin, AP HP, Fac Med Paris Descartes,Serv Pneumol, F-75679 Paris 14, FranceUniv Paris 05, Hop Cochin, AP HP, Fac Med Paris Descartes,Serv Pneumol, F-75679 Paris 14, France
Natali, D.
Tuiliez, M.
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Univ Paris 05, Fac Med Paris Descartes, Serv Anat Pathol, Hop Cochin, F-75014 Paris, FranceUniv Paris 05, Hop Cochin, AP HP, Fac Med Paris Descartes,Serv Pneumol, F-75679 Paris 14, France
Tuiliez, M.
Burgel, P. -R.
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Univ Paris 05, Hop Cochin, AP HP, Fac Med Paris Descartes,Serv Pneumol, F-75679 Paris 14, FranceUniv Paris 05, Hop Cochin, AP HP, Fac Med Paris Descartes,Serv Pneumol, F-75679 Paris 14, France
Burgel, P. -R.
Mouthon, L.
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Univ Paris 05, Hop Cochin, Fac Med Paris Descartes, Ctr Reference Pour Vasc Necrosantes & Sclerodermi, F-75014 Paris, FranceUniv Paris 05, Hop Cochin, AP HP, Fac Med Paris Descartes,Serv Pneumol, F-75679 Paris 14, France
Mouthon, L.
Dusser, D.
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Univ Paris 05, Hop Cochin, AP HP, Fac Med Paris Descartes,Serv Pneumol, F-75679 Paris 14, FranceUniv Paris 05, Hop Cochin, AP HP, Fac Med Paris Descartes,Serv Pneumol, F-75679 Paris 14, France
Dusser, D.
Montani, D.
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Univ Paris 05, Hop Cochin, AP HP, Fac Med Paris Descartes,Serv Pneumol, F-75679 Paris 14, FranceUniv Paris 05, Hop Cochin, AP HP, Fac Med Paris Descartes,Serv Pneumol, F-75679 Paris 14, France