Reply to 'F508del-CFTR is not corrected by thymosin α1'

被引：2

作者：

Romani, Luigina ^{[1
]}

Stincardini, Claudia ^{[1
]}

Giovagnoli, Stefano ^{[2
]}

Paci, Maurizio ^{[3
]}

Villella, Valeria R. ^{[4
]}

Sforna, Luigi ^{[1
]}

Renga, Giorgia ^{[1
]}

Bellet, Marina M. ^{[1
]}

Costantini, Claudio ^{[1
]}

Puccetti, Paolo ^{[1
]}

Kroemer, Guido ^{[5
,6
,7
,8
]}

Maiuri, Luigi ^{[4
,9
]}

Pessia, Mauro ^{[1
]}

Goldstein, Allan ^{[10
]}

Garaci, Enrico ^{[11
]}

机构：

[1] Univ Perugia, Dept Expt Med, Perugia, Italy

[2] Univ Perugia, Dept Pharmaceut Sci, Perugia, Italy

[3] Univ Roma Tor Vergata, Dept Chem Sci & Technol, Rome, Italy

[4] Ist Sci San Raffaele, Div Genet & Cell Biol, European Inst Res Cyst Fibrosis, Milan, Italy

[5] Univ Paris 05, INSERM, U1138, Ctr Rech Cordeliers, Paris, France

[6] Inst Gustave Roussy, Metab & Cell Biol Platforms, Villejuif, France

[7] Hop Europeen Georges Pompidou, AP HP, Pole Biol, Paris, France

[8] Karolinska Univ Hosp, Dept Womens & Childrens Hlth, Karolinska Inst, Stockholm, Sweden

[9] Univ Piemonte Orientale, Dept Hlth Sci, Novara, Italy

[10] George Washington Univ, Sch Med & Hlth Sci, Dept Biochem & Mol Med, Washington, DC 20052 USA

[11] Univ San Raffaele, Rome, Italy

来源：

NATURE MEDICINE | 2018年 / 24卷 / 07期

关键词：

CYSTIC-FIBROSIS; MODEL; INFLAMMATION; AUTOPHAGY;

D O I：

10.1038/s41591-018-0080-0

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：891 / 893

页数：4

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