Antenatal solitary intestinal fibromatosis

被引:0
|
作者
Duval, H
Jouan, H
Loeuillet, L
Azzis, O
Vongsavanthong, S
Coindre, JM
机构
[1] CHU Pontchaillou, Dept Anat & Cytol Pathol, F-35000 Rennes, France
[2] CHU Pontchaillou, Clin Chirurg Infantile, F-35000 Rennes, France
[3] Cabinet Gynecol, Pontivy, France
[4] Inst Bergonie, Serv Anat Pathol, Bordeaux, France
关键词
intestinal fibromatosis; neonatal fibromatosis; neonatal intestinal obstruction;
D O I
暂无
中图分类号
R36 [病理学];
学科分类号
100104 ;
摘要
Solitary intestinal fibromatosis (SIF) is rare. Only 16 cases have been described in the new-born and infancy. We describe a new case of SIF with an unusual presentation including abnormal antenatal echographic findings. SIF was diagnosed at 2 months age when the child developed an intestinal obstruction. Differential diagnosis and review of literature are discussed. This lesion has an excellent prognosis when it is completely excised.
引用
收藏
页码:169 / 172
页数:4
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