Pediatric Gastrointestinal PEComas: A Diagnostic Challenge

被引:5
|
作者
Pizzi, Marco [1 ]
di Lorenzo, Ida [2 ]
d'Amore, Emanuele S. [3 ]
D'Angelo, Paolo [4 ]
Alaggio, Rita [1 ]
机构
[1] Univ Padua, Dept Med DIMED, Gen Pathol & Cytopathol Unit, Padua, Italy
[2] Di Cristina & Benfratelli Hosp, ARNAS Civ, Pathol Unit, Palermo, Italy
[3] San Bortolo Hosp, Dept Pathol, Vicenza, Italy
[4] Di Cristina & Benfratelli Hosp, ARNAS Civ, Pediat Hematol & Oncol Unit, Palermo, Italy
关键词
clear cell sarcoma; gastrointestinal mesenchymal tumors; PEComa; pediatric pathology; SOX10; CHILDREN; TUMORS;
D O I
10.2350/14-06-1501-CR.1
中图分类号
R36 [病理学];
学科分类号
100104 ;
摘要
Perivascular epithelioid cell tumors (PEComas) in the pediatric population are very rare and frequently arise in the gastrointestinal tract. These tumors are characterized by variable morphological and immunohistochemical features, which may pose significant problems in differential diagnosis with other gastrointestinal mesenchymal tumors in pediatric patients. In presenting an unusual pediatric case of gastrointestinal PEComa, we also discuss the possible differential diagnosis of this rare entity.
引用
收藏
页码:406 / 408
页数:3
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