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Granulomatous myositis, primary biliary cirrhosis, pancytopenia, and thymoma
被引:0
|作者:
Herrmann, DN
Blaivas, M
Wald, JJ
Feldman, EL
机构:
[1] Univ Rochester, Dept Neurol, Rochester, NY 14642 USA
[2] Univ Michigan, Dept Pathol, Ann Arbor, MI 48109 USA
[3] Univ Michigan, Dept Neurol, Ann Arbor, MI USA
关键词:
corticosteroids;
granulomatous myopathy;
paraneoplastic syndrome;
primary biliary cirrhosis;
thymoma;
D O I:
10.1002/1097-4598(200007)23:7<1133::AID-MUS20>3.3.CO;2-5
中图分类号:
R74 [神经病学与精神病学];
学科分类号:
摘要:
Granulomatous myopathies are rare. Most cases are associated with sarcoidosis. We report a case of granulomatous myopathy associated with primary biliary cirrhosis, pancytopenia, and thymoma. The literature in regard to granulomatous myopathy and its pathogenesis is reviewed. Intermittent pulsed intravenous methylprednisolone may be useful as maintenance therapy for granulomatous myopathy and other neuromuscular syndromes for patients intolerant of oral corticosteroids. (C) 2000 John Wiley & Sons, Inc.
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页码:1133 / 1136
页数:4
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