Hedinger syndrome refers to carcinoid valvular heart disease. The disease is believed to be triggered by vasoactive substances that result in valvular fibrosis. It classically occurs in patients with metastatic carcinoid and preferentially involves the right sided cardiac valves. Affected valves become thickened and retracted, exhibiting regurgitation and sometimes, stenosis. Echocardiography is recommended in patients with carcinoid syndrome and a follow up study is advisable in those who develop a murmur or other symptoms or signs of valvular heart disease. For appropriately selected patients, valve replacement surgery appears to improve outcomes. (C) 2015 Elsevier Ltd. All rights reserved.
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Univ Calif San Diego, Sulpizio Cardiovasc Ctr, San Diego, CA 92103 USA
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Univ Calif Los Angeles, David Geffen Sch Med, 200 Med Plz,Ste B114, Los Angeles, CA 90095 USAUniv Calif Los Angeles, David Geffen Sch Med, 200 Med Plz,Ste B114, Los Angeles, CA 90095 USA
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Univ Calif Los Angeles, Dept Radiol, Los Angeles, CA USAUniv Calif Los Angeles, David Geffen Sch Med, 200 Med Plz,Ste B114, Los Angeles, CA 90095 USA
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Univ Calif Los Angeles, Dept Radiol, Los Angeles, CA USAUniv Calif Los Angeles, David Geffen Sch Med, 200 Med Plz,Ste B114, Los Angeles, CA 90095 USA
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