Erdheim-Chester disease (ECD) is a rare non-Langerhans histiocytosis of unknown etiology, it is characterized by organ infiltration of foamy histiocytes. Diagnosis of ECD involves the analysis of histiocytes in tissue biopsies: these are typically CD68+ CD1a-. These characteristic histiocytes may be found in almost any tissue in cases of ECD. We present an interesting case of ECD that was presented by spontaneous pneumothorax and neurological involvement.
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Univ Autonoma Barcelona, Vall dHebron Gen Hosp, Dept Internal Med, Barcelona 08035, SpainUniv Autonoma Barcelona, Vall dHebron Gen Hosp, Dept Internal Med, Barcelona 08035, Spain
Juanos-Iborra, Montserrat
Solanich-Moreno, Javier
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IDIBELL, Bellvitge Hosp, Dept Internal Med, Barcelona, SpainUniv Autonoma Barcelona, Vall dHebron Gen Hosp, Dept Internal Med, Barcelona 08035, Spain
Solanich-Moreno, Javier
Selva-O'Callaghan, Albert
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Univ Autonoma Barcelona, Vall dHebron Gen Hosp, Dept Internal Med, Barcelona 08035, SpainUniv Autonoma Barcelona, Vall dHebron Gen Hosp, Dept Internal Med, Barcelona 08035, Spain
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Hop La Pitie Salpetriere, AP HP, Dept Internal Med, Paris, France
Hop La Pitie Salpetriere, AP HP, French Reference Ctr Rare Autoimmune & Syst Dis, Paris, France
Univ Paris 06, Paris, FranceHop La Pitie Salpetriere, AP HP, Dept Internal Med, Paris, France
Haroche, Julien
Arnaud, Laurent
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Hop La Pitie Salpetriere, AP HP, Dept Internal Med, Paris, France
Hop La Pitie Salpetriere, AP HP, French Reference Ctr Rare Autoimmune & Syst Dis, Paris, France
INSERM, UMR S 945, Paris, FranceHop La Pitie Salpetriere, AP HP, Dept Internal Med, Paris, France
Arnaud, Laurent
Amoura, Zahir
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Hop La Pitie Salpetriere, AP HP, Dept Internal Med, Paris, France
Hop La Pitie Salpetriere, AP HP, French Reference Ctr Rare Autoimmune & Syst Dis, Paris, France
Univ Paris 06, Paris, France
INSERM, UMR S 945, Paris, FranceHop La Pitie Salpetriere, AP HP, Dept Internal Med, Paris, France
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Hop La Pitie Salpetriere, AP HP, Dept Internal Med, Paris, France
Hop La Pitie Salpetriere, AP HP, French Reference Ctr Rare Autoimmune & System Dis, Paris, France
Univ Paris 06, Paris, FranceHop La Pitie Salpetriere, AP HP, Dept Internal Med, Paris, France
Haroche, Julien
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Arnaud, Laurent
Cohen-Aubart, Fleur
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Hop La Pitie Salpetriere, AP HP, Dept Internal Med, Paris, France
Hop La Pitie Salpetriere, AP HP, French Reference Ctr Rare Autoimmune & System Dis, Paris, France
Univ Paris 06, Paris, FranceHop La Pitie Salpetriere, AP HP, Dept Internal Med, Paris, France
Cohen-Aubart, Fleur
Hervier, Baptiste
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Hop La Pitie Salpetriere, AP HP, Dept Internal Med, Paris, France
Hop La Pitie Salpetriere, AP HP, French Reference Ctr Rare Autoimmune & System Dis, Paris, France
Univ Paris 06, Paris, FranceHop La Pitie Salpetriere, AP HP, Dept Internal Med, Paris, France
Hervier, Baptiste
Charlotte, Frederic
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Univ Paris 06, Paris, France
Hop La Pitie Salpetriere, AP HP, Dept Anatomopathol, Paris, FranceHop La Pitie Salpetriere, AP HP, Dept Internal Med, Paris, France
Charlotte, Frederic
Emile, Jean-Francois
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Hop La Pitie Salpetriere, AP HP, Dept Anatomopathol, Paris, France
Univ Versailles, Ambroise Pare Hosp, AP HP, Boulogne, FranceHop La Pitie Salpetriere, AP HP, Dept Internal Med, Paris, France
Emile, Jean-Francois
Amoura, Zahir
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Hop La Pitie Salpetriere, AP HP, Dept Internal Med, Paris, France
Hop La Pitie Salpetriere, AP HP, French Reference Ctr Rare Autoimmune & System Dis, Paris, France
Univ Paris 06, Paris, FranceHop La Pitie Salpetriere, AP HP, Dept Internal Med, Paris, France