Fibrillin-1 protein in tight skin mice and scleroderma

被引：6
|
作者：
Bona, C [1 ]
Saito, S [1 ]
机构：
[1] CUNY Mt Sinai Sch Med, Dept Microbiol, New York, NY 10029 USA
来源：
CLINICAL REVIEWS IN ALLERGY & IMMUNOLOGY | 2000年 / 18卷 / 01期
关键词：
D O I：
10.1385/CRIAI:18:1:119
中图分类号：
R392 [医学免疫学];
学科分类号：
100102 ;
摘要：
[No abstract available]
引用
收藏
页码：119 / 126
页数：8
相关论文
共 50 条
  • [31] Initial mechanisms in fibrillin-1 assembly
    El-Hallous, E.
    Tiedemann, K.
    Hubmacher, D.
    Weiss, A.
    Sasaki, T.
    Davis, E. C.
    Reinhardt, D. P.
    MATRIX BIOLOGY, 2006, 25 : S19 - S19
  • [32] Fibrillin-1 regulates the bioavailability of TGFβ1
    Chaudhry, Shazia S.
    Cain, Stuart A.
    Morgan, Amanda
    Dallas, Sarah L.
    Shuttleworth, C. Adrian
    Kielty, Cay M.
    JOURNAL OF CELL BIOLOGY, 2007, 176 (03): : 355 - 367
  • [33] Fibrillin-1 regulates the bioavailability of TGFβ1
    Chaudhry, S. S.
    Cain, S. A.
    Morgan, A.
    Dallas, S. L.
    Shuttleworth, C. A.
    Kielty, C. M.
    INTERNATIONAL JOURNAL OF EXPERIMENTAL PATHOLOGY, 2007, 88 (06) : A92 - A93
  • [34] Fibrillin-1 G234D mutation in the hybrid1 domain causes tight skin associated with dysregulated elastogenesis and increased collagen cross-linking in mice
    Hossain, A. S. M. Sakhawat
    Clarin, Maria Thea Rane Dela Cruz
    Kimura, Kenichi
    Biggin, George
    Taga, Yuki
    Uto, Koichiro
    Yamagishi, Ayana
    Motoyama, Eri
    Narenmandulaa
    Mizuno, Kazunori
    Nakamura, Chikashi
    Asano, Keiichi
    Ohtsuki, Sumio
    Nakamura, Tomoyuki
    Kanki, Sachiko
    Baldock, Clair
    Raja, Erna
    Yanagisawa, Hiromi
    MATRIX BIOLOGY, 2025, 135 : 24 - 38
  • [35] Fibrillin-1 mutants in Marfan syndrome and tight-skin mouse antagonistically affect expression of CCN3 and MAGP-2: Novel molecular insights into extracellular matrix regulation by fibrillin-1 in connective tissue.
    Lemaire, Raphael
    Bayle, Julie
    Lafyatis, Robert
    ARTHRITIS AND RHEUMATISM, 2006, 54 (09): : S729 - S730
  • [36] Reduction and fragmentation of elastic fibers in the skin of obese mice is associated with altered mRNA expression levels of fibrillin-1 and neprilysin
    Makihara, Hiroko
    Hidaka, Moeko
    Sakai, Yui
    Horie, Yoshiko
    Mitsui, Hideaki
    Ohashi, Kenichi
    Goshima, Yoshio
    Akase, Tomoko
    CONNECTIVE TISSUE RESEARCH, 2017, 58 (05) : 479 - 486
  • [37] Abnormalities in fibrillin-1 containing microfibrils in fibroblast cultures from systemic sclerosis (scleroderma) patients.
    Wallis, DD
    Tan, FK
    Kielty, CM
    Arnett, FC
    Milewicz, DM
    ARTHRITIS AND RHEUMATISM, 1999, 42 (09): : S169 - S169
  • [38] Extracellular Regulation of Bone Morphogenetic Protein Activity by the Microfibril Component Fibrillin-1
    Wohl, Alexander P.
    Troilo, Helen
    Collins, Richard F.
    Baldock, Clair
    Sengle, Gerhard
    JOURNAL OF BIOLOGICAL CHEMISTRY, 2016, 291 (24) : 12732 - 12746
  • [39] Defective calcium binding to fibrillin-1: Consequence of an N2144S change for fibrillin-1 structure and function
    Kettle, S
    Yuan, XM
    Grundy, G
    Knott, V
    Downing, AK
    Handford, PA
    JOURNAL OF MOLECULAR BIOLOGY, 1999, 285 (03) : 1277 - 1287
  • [40] Fibrillin-1: Organization in microfibrils and structural properties
    Reinhardt, DP
    Keene, DR
    Corson, GM
    Poschl, E
    Bachinger, HP
    Gambee, JE
    Sakai, LY
    JOURNAL OF MOLECULAR BIOLOGY, 1996, 258 (01) : 104 - 116
12345