Osteochondritis dissecans in a patient with hyperimmunoglobulin E syndrome

被引:0
|
作者
Kiliç, SS
Sanal, Ö
Tezcan, I
Ersoy, F
机构
[1] Uludag Univ, Fac Med, Dept Pediat, Bursa, Turkey
[2] Hacettepe Univ, Fac Med, Dept Pediat, Immunol Unit, TR-06100 Ankara, Turkey
关键词
bone abnormalities; hyperimmunoglobulin E syndrome; osteochondritis dissecans; osteopenia;
D O I
暂无
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Hyperimmunoglobulin E syndrome (hyper-IgE) is a rare immunodeficiency disease associated with recurrent pyogenic infections, chronic eczematoid dermatitis and osteopenia. We present here a 13-year-old girl with hyperimmunoglobulin E syndrome, who developed osteochondritis dissecans (OCD) of the lateral femoral condyle, which is rare. Osteopenia, which is frequently associated with hyper IgE, may predispose the patient to the development of OCD.
引用
收藏
页码:357 / 359
页数:3
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