Nutrition Management of Pediatric Patients Who Have Cystic Fibrosis

被引:14
|
作者
Michel, Suzanne H. [1 ]
Maqbool, Asim [2 ]
Hanna, Maria D. [1 ]
Mascarenhas, Maria [2 ]
机构
[1] Univ Penn, Sch Med, Childrens Hosp Philadelphia, Dept Clin Nutr, Philadelphia, PA 19104 USA
[2] Univ Penn, Sch Med, Childrens Hosp Philadelphia, Div Gastroenterol Hepatol & Nutr, Philadelphia, PA 19104 USA
关键词
Cystic fibrosis; Nutrition; Vitamins; Minerals; Energy; Protein; Fatty acids; Pancreatic; Enzymes; RESTING ENERGY-EXPENDITURE; VITAMIN-E-DEFICIENCY; FATTY-ACID STATUS; COPPER ENZYME-ACTIVITIES; LUNG-DISEASE SEVERITY; SERUM RETINOL LEVELS; PREADOLESCENT CHILDREN; IRON-DEFICIENCY; DIETARY SUPPLEMENTATION; PULMONARY-FUNCTION;
D O I
10.1016/j.pcl.2009.06.008
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Since the identification of cystic fibrosis (CF) in the 1940s, nutrition care of patients who have CIF has been a challenge. Through optimal caloric intake and careful management of malabsorption, patients are expected to meet genetic potential for growth. Yet factors beyond malabsorption, including nutrient activity at the cellular level, may influence growth and health. This article reviews nutrition topics frequently discussed in relationship to CF and presents intriguing new information describing nutrients currently being studied for their impact on overall health of patients who have CF.
引用
收藏
页码:1123 / +
页数:20
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