Nutrition Management of Pediatric Patients Who Have Cystic Fibrosis

被引:14
|
作者
Michel, Suzanne H. [1 ]
Maqbool, Asim [2 ]
Hanna, Maria D. [1 ]
Mascarenhas, Maria [2 ]
机构
[1] Univ Penn, Sch Med, Childrens Hosp Philadelphia, Dept Clin Nutr, Philadelphia, PA 19104 USA
[2] Univ Penn, Sch Med, Childrens Hosp Philadelphia, Div Gastroenterol Hepatol & Nutr, Philadelphia, PA 19104 USA
关键词
Cystic fibrosis; Nutrition; Vitamins; Minerals; Energy; Protein; Fatty acids; Pancreatic; Enzymes; RESTING ENERGY-EXPENDITURE; VITAMIN-E-DEFICIENCY; FATTY-ACID STATUS; COPPER ENZYME-ACTIVITIES; LUNG-DISEASE SEVERITY; SERUM RETINOL LEVELS; PREADOLESCENT CHILDREN; IRON-DEFICIENCY; DIETARY SUPPLEMENTATION; PULMONARY-FUNCTION;
D O I
10.1016/j.pcl.2009.06.008
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Since the identification of cystic fibrosis (CF) in the 1940s, nutrition care of patients who have CIF has been a challenge. Through optimal caloric intake and careful management of malabsorption, patients are expected to meet genetic potential for growth. Yet factors beyond malabsorption, including nutrient activity at the cellular level, may influence growth and health. This article reviews nutrition topics frequently discussed in relationship to CF and presents intriguing new information describing nutrients currently being studied for their impact on overall health of patients who have CF.
引用
下载
收藏
页码:1123 / +
页数:20
相关论文
共 50 条
  • [1] Nutrition for Pregnant Women Who Have Cystic Fibrosis
    Michel, Suzanne H.
    Mueller, Donna H.
    JOURNAL OF THE ACADEMY OF NUTRITION AND DIETETICS, 2012, 112 (12) : 1943 - 1948
  • [2] IMPROVING NUTRITION FOR PEDIATRIC CYSTIC FIBROSIS PATIENTS
    Ramirez, I
    Nasr, S. Z.
    Filbrun, A.
    PEDIATRIC PULMONOLOGY, 2012, 47 : 406 - 406
  • [3] IMPROVING NUTRITION IN PEDIATRIC CYSTIC FIBROSIS PATIENTS
    Muceus, K.
    Viles, T.
    Walter, J. N.
    PEDIATRIC PULMONOLOGY, 2015, 50 : 405 - 405
  • [4] HOME PARENTERAL NUTRITION IN PEDIATRIC CYSTIC FIBROSIS PATIENTS
    Moreno Villares, J. M.
    Lopez Manzanares, J. Manzanares
    Valero Zanuy, Ma A.
    Leon Sanz, M.
    NUTRICION HOSPITALARIA, 2009, 24 (06) : 761 - 762
  • [5] Nutrition in the management of cystic fibrosis
    Dowsett, J
    NUTRITION REVIEWS, 1996, 54 (01) : 31 - 33
  • [6] Validation of a Nutrition Screening Tool for Pediatric Patients with Cystic Fibrosis
    Souza dos Santos Simon, Miriam Isabel
    Forte, Gabriele Carra
    Pereira, Juliane da Silva
    Andrade Procianoy, Elenara da Fonseca
    Drehmer, Michele
    JOURNAL OF THE ACADEMY OF NUTRITION AND DIETETICS, 2016, 116 (05) : 813 - 818
  • [7] Advances in lung transplantation for patients who have cystic fibrosis
    Goldberg, Hilary J.
    Deykin, Aaron
    CLINICS IN CHEST MEDICINE, 2007, 28 (02) : 445 - +
  • [8] UTLIZATION OF TOTAL PARENTERAL NUTRITION AND INTRALIPIDS IN PEDIATRIC CYSTIC FIBROSIS PATIENTS
    Ghazala, Z. B.
    Thakuria, K.
    Shaw, K.
    Sathe, M. N.
    PEDIATRIC PULMONOLOGY, 2015, 50 : 403 - 404
  • [9] Transition and transfer of patients who have cystic fibrosis to adult care
    Parker, H. Worth
    CLINICS IN CHEST MEDICINE, 2007, 28 (02) : 423 - +
  • [10] Nutrition management in adults with cystic fibrosis
    Shape, Jessica M.
    Sala, Marc A.
    NUTRITION IN CLINICAL PRACTICE, 2022, 37 (02) : 256 - 264