Kaposiform hemangioendothelioma is a rare vascular neoplasm in children often associated with Kasabach-Merritt syndrome. The tumor usually presents in retroperitoneal location and is rarely present at birth. Cutaneous lesions manifest after birth and must be clinically differentiated from infantile hemangiomas and diffuse neonatal hemangiomatosis. Histologically, it bears similarities with Kaposi sarcoma. We present a case of congenital cutaneous multifocal kaposiform hemangioendothelioma (KHE).
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Univ Clin Navarra, Dept Dermatol, Marquesado de Santa Marta St 1, Madrid 28027, SpainUniv Clin Navarra, Dept Dermatol, Marquesado de Santa Marta St 1, Madrid 28027, Spain
Ivars, Marta
Triana, Paloma
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Univ Hosp La Paz, Dept Pediat Surg, Madrid, SpainUniv Clin Navarra, Dept Dermatol, Marquesado de Santa Marta St 1, Madrid 28027, Spain
Triana, Paloma
Lopez-Gutierrez, Juan Carlos
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Univ Hosp La Paz, Dept Pediat Surg, Madrid, SpainUniv Clin Navarra, Dept Dermatol, Marquesado de Santa Marta St 1, Madrid 28027, Spain
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Hosp Gen Univ Gregorio Maranon, Dept Dermatol, C Doctor Esquerdo 46, Madrid 28007, SpainHosp Gen Univ Gregorio Maranon, Sect Neonatol, Dept Pediat, Madrid, Spain
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Univ Tokyo, Grad Sch Med, Dept Pathol, Tokyo 1130033, Japan
Tokyo Med Univ, Dept Mol Pathol, Tokyo 1608402, JapanUniv Tokyo, Grad Sch Med, Dept Pathol, Tokyo 1130033, Japan
Nakaya, Takeo
Morita, Kiyoko
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Univ Tokyo, Grad Sch Med, Dept Pediat, Tokyo 1130033, JapanUniv Tokyo, Grad Sch Med, Dept Pathol, Tokyo 1130033, Japan
Morita, Kiyoko
Kurata, Atsushi
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Tokyo Med Univ, Dept Mol Pathol, Tokyo 1608402, JapanUniv Tokyo, Grad Sch Med, Dept Pathol, Tokyo 1130033, Japan
Kurata, Atsushi
Ushiku, Tetsuo
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Univ Tokyo, Grad Sch Med, Dept Pathol, Tokyo 1130033, JapanUniv Tokyo, Grad Sch Med, Dept Pathol, Tokyo 1130033, Japan
Ushiku, Tetsuo
Igarashi, Takashi
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Univ Tokyo, Grad Sch Med, Dept Pediat, Tokyo 1130033, JapanUniv Tokyo, Grad Sch Med, Dept Pathol, Tokyo 1130033, Japan
Igarashi, Takashi
Kuroda, Masahiko
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Tokyo Med Univ, Dept Mol Pathol, Tokyo 1608402, JapanUniv Tokyo, Grad Sch Med, Dept Pathol, Tokyo 1130033, Japan
Kuroda, Masahiko
Fukayama, Masashi
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Univ Tokyo, Grad Sch Med, Dept Pathol, Tokyo 1130033, JapanUniv Tokyo, Grad Sch Med, Dept Pathol, Tokyo 1130033, Japan
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Natl Ctr Child Hlth & Dev, Childrens Canc Ctr, Setagaya Ku, Tokyo, JapanNatl Ctr Child Hlth & Dev, Childrens Canc Ctr, Setagaya Ku, Tokyo, Japan
Uno, Teruaki
Ito, Shuichi
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Natl Ctr Child Hlth & Dev, Div Nephrol & Rheumatol, Setagaya Ku, Tokyo, JapanNatl Ctr Child Hlth & Dev, Childrens Canc Ctr, Setagaya Ku, Tokyo, Japan
Ito, Shuichi
Nakazawa, Atsuko
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Natl Ctr Child Hlth & Dev, Dept Pathol, Setagaya Ku, Tokyo, JapanNatl Ctr Child Hlth & Dev, Childrens Canc Ctr, Setagaya Ku, Tokyo, Japan
Nakazawa, Atsuko
Miyazaki, Osamu
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Natl Ctr Child Hlth & Dev, Dept Radiol, Setagaya Ku, Tokyo, JapanNatl Ctr Child Hlth & Dev, Childrens Canc Ctr, Setagaya Ku, Tokyo, Japan
Miyazaki, Osamu
Mori, Tetsuya
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Natl Ctr Child Hlth & Dev, Childrens Canc Ctr, Setagaya Ku, Tokyo, JapanNatl Ctr Child Hlth & Dev, Childrens Canc Ctr, Setagaya Ku, Tokyo, Japan
Mori, Tetsuya
Terashima, Keita
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Natl Ctr Child Hlth & Dev, Childrens Canc Ctr, Setagaya Ku, Tokyo, JapanNatl Ctr Child Hlth & Dev, Childrens Canc Ctr, Setagaya Ku, Tokyo, Japan