Neurological Manifestations in Two Cases of En Coup De Sabre

Scleroderma En Coup de Sabre (ECDS) is a form of localised scleroderma that primarily develops in the younger population, usually before the age of 18 years and occurs on the scalp or forehead. In localised scleroderma, en coup de sabre, many studies and case reports describe neurological signs and symptoms. Two patients with the disease are reported here who were noted to have brain cysts by neuroimaging. It is important to specifically inquire about neurological symptoms and signs in the history and examination, respectively, and to consider neuroimaging in patients with scleroderma en coup de sabre to diagnose and treat neurological complications.