Marfan syndrome

被引:0
|
作者
Vatutin, N. T. [1 ]
Sklyannaya, E. V. [1 ]
Keting, E. V. [1 ]
机构
[1] M Gorky Donetsk State Med Univ, VK Gusak Res Inst Crit Care & Surg, Donetsk, Ukraine
关键词
Marfan syndrome; aortic aneurysm; dissection;
D O I
暂无
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Marfan syndrome is a hereditary disease of connective tissue with predominant involvement of cardiovascular system, skeleton and eyes. Timely diagnosis and adequate management can substantially decrease mortality in this condition. The review summarizes data of clinical observations and studies of etiology, pathogenesis, diagnosis and treatment of Marfan syndrome.
引用
收藏
页码:92 / 98
页数:7
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