机构:
M Gorky Donetsk State Med Univ, VK Gusak Res Inst Crit Care & Surg, Donetsk, UkraineM Gorky Donetsk State Med Univ, VK Gusak Res Inst Crit Care & Surg, Donetsk, Ukraine
Vatutin, N. T.
[1
]
Sklyannaya, E. V.
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M Gorky Donetsk State Med Univ, VK Gusak Res Inst Crit Care & Surg, Donetsk, UkraineM Gorky Donetsk State Med Univ, VK Gusak Res Inst Crit Care & Surg, Donetsk, Ukraine
Sklyannaya, E. V.
[1
]
Keting, E. V.
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M Gorky Donetsk State Med Univ, VK Gusak Res Inst Crit Care & Surg, Donetsk, UkraineM Gorky Donetsk State Med Univ, VK Gusak Res Inst Crit Care & Surg, Donetsk, Ukraine
Keting, E. V.
[1
]
机构:
[1] M Gorky Donetsk State Med Univ, VK Gusak Res Inst Crit Care & Surg, Donetsk, Ukraine
Marfan syndrome is a hereditary disease of connective tissue with predominant involvement of cardiovascular system, skeleton and eyes. Timely diagnosis and adequate management can substantially decrease mortality in this condition. The review summarizes data of clinical observations and studies of etiology, pathogenesis, diagnosis and treatment of Marfan syndrome.
机构:
Sanjay Gandhi Post Grad Inst Med Sci, Dept Genet, Lucknow 226014, Uttar Pradesh, IndiaSanjay Gandhi Post Grad Inst Med Sci, Dept Genet, Lucknow 226014, Uttar Pradesh, India
Kumar, Ashok
Agarwal, Sarita
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Sanjay Gandhi Post Grad Inst Med Sci, Dept Genet, Lucknow 226014, Uttar Pradesh, IndiaSanjay Gandhi Post Grad Inst Med Sci, Dept Genet, Lucknow 226014, Uttar Pradesh, India