Primary extraskeletal Ewing sarcoma of the sinonasal tract: a rare case report and review of the literature

Purpose: Extraskeletal Ewing sarcoma (EES) is a rare, round-cell malignant neoplasm that mostly manifests as a large and bulky soft-tissue mass. EES is most commonly found in the paravertebral region, extremities, chest wall, retroperitoneum, pelvis and hip. EES can occur in the head and neck. However such locations are considered to be rare for this type of malignant neoplasm. Methods: We report a 41 years female diagnosed with EES, and performed a brief review about the clinical features and diagnostic strategies of the EES. Results: The CT and MRI examination reveals a mass in the nasal cavity and paranasal sinuses, and the pathological examination supported the diagnosis of EES. Conclusions: Primary Ewing's sarcoma must be considered when the expansile nasal mass is detected with extensive invasion into adjacent structures and bony destructive changes, although which is a very rare condition.