Pre-excitation syndrome secondary to cardiac rhabdomyomas in tuberous sclerosis

被引:25
|
作者
Mas, C [1 ]
Penny, DJ [1 ]
Menahem, S [1 ]
机构
[1] Monash Univ, Monash Med Ctr, Dept Paediat, Ctr Heart & Chest Res, Clayton, Vic 3168, Australia
关键词
hydrops fetalis; pre-excitation syndrome; rhabdomyoma; supraventricular tachycardia; tuberous sclerosis;
D O I
10.1046/j.1440-1754.2000.00443.x
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Rhabdomyomas are not uncommon in infants with tuberous sclerosis. We describe a neonate who presented with hydrops fetalis arising from a tachyarrhythmia during fetal Life related to rhabdomyomas. After reversion of the arrhythmia, pre-excitation was noted on an intel val electrocardiogram. Following regression of the tumours, the delta wave disappeared with no further arrhythmias noted.
引用
收藏
页码:84 / 86
页数:3
相关论文
共 50 条
  • [41] Tuberous sclerosis, cardiac rhabdomyomas and competitive Paralympic sports activity: a case report
    Palmieri, Vincenzo
    Cuccaro, Francesco
    Orvieto, Sebastiano
    Bianco, Massimiliano
    Zeppilli, Paolo
    MEDICINA DELLO SPORT, 2017, 70 (01) : 104 - 108
  • [42] THE CLINICAL-SIGNIFICANCE OF THE PRE-EXCITATION SYNDROME
    NIKITIN, AV
    GUSMANOV, VA
    KLINICHESKAYA MEDITSINA, 1988, 66 (11): : 39 - 45
  • [43] THE EXERCISE STRESS TEST IN THE PRE-EXCITATION SYNDROME
    BIANCONI, L
    BOCCARDI, L
    GHILARDI, P
    PENNESTRI, F
    RULLI, FG
    MINERVA CARDIOANGIOLOGICA, 1982, 30 (09): : 453 - 460
  • [44] A case report of tuberous sclerosis with cardiac rhabdomyomas diagnosed antenatally by fetal echocardiography
    Gurses, Dolunay
    Levent, Ertuerk
    Ulger, Zulal
    Ozyurek, A. Ruhi
    TURK PEDIATRI ARSIVI-TURKISH ARCHIVES OF PEDIATRICS, 2009, 44 (04): : 146 - 148
  • [45] Effect and Complications of Everolimus Use for Giant Cardiac Rhabdomyomas with Neonatal Tuberous Sclerosis
    Shibata, Yuka
    Maruyama, Hidehiko
    Hayashi, Taiyu
    Ono, Hiroshi
    Wada, Yuka
    Fujinaga, Hideshi
    Fujino, Shuhei
    Nagasawa, Junko
    Amari, Shoichiro
    Tsukamoto, Keiko
    Ito, Yushi
    AJP REPORTS, 2019, 9 (03): : E213 - E217
  • [46] PRE-EXCITATION SYNDROME IN IDENTICAL-TWINS
    MISPIRETA, JL
    CARDENAS, M
    ATTIE, F
    MARTINEZRIOS, MA
    MEDRANO, GA
    ARCHIVOS DEL INSTITUTO DE CARDIOLOGIA DE MEXICO, 1976, 46 (01): : 3 - 11
  • [47] An Unusual Case of Large, Multifocal Cardiac Rhabdomyomas in Suspected Fetal Tuberous Sclerosis
    Sherani, Muhammad Shaheer Khan
    Marney, Michael
    Park, Jin
    SOUTHERN MEDICAL JOURNAL, 2021, 114 (08)
  • [48] Cardiac rhabdomyomas associated with tuberous sclerosis complex in children From presentation to outcome
    Shen, Q.
    Shen, J.
    Qiao, Z.
    Yao, Q.
    Huang, G.
    Hu, X.
    HERZ, 2015, 40 (04) : 675 - 678
  • [49] Multiple cardiac rhabdomyomas not associated with tuberous sclerosis in a dizygotic twins: a case report
    Koji Yamamoto
    Yohei Maki
    Yuichiro Sato
    Hiroyuki Tanaka
    Tsuyoshi Fukushima
    Junko Ushijima
    Seishi Furukawa
    Hiroshi Sameshima
    Hiroaki Kataoka
    Journal of Medical Case Reports, 15
  • [50] PRE-EXCITATION SYNDROME (REVIEW OF 235 CASES)
    PAJARONLOPEZ, A
    POVEDASI.J
    MEDRANO, GA
    ARCHIVOS DEL INSTITUTO DE CARDIOLOGIA DE MEXICO, 1973, 43 (06): : 826 - 836