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- [21] Effects of Lumacaftor-Ivacaftor Therapy on CFTR Function in Phe508del Homozygous Patients with Cystic FibrosisEUROPEAN RESPIRATORY JOURNAL, 2018, 52Graeber, Simon论文数: 0 引用数: 0 h-index: 0机构: Heidelberg Univ, Dept Translat Pulmonol, Translat Lung Res Ctr Heidelberg TLRC, German Ctr Lung Res DZL, Heidelberg, Germany Heidelberg Univ, Dept Translat Pulmonol, Translat Lung Res Ctr Heidelberg TLRC, German Ctr Lung Res DZL, Heidelberg, GermanyDopfer, Christian论文数: 0 引用数: 0 h-index: 0机构: Hannover Med Sch, Clin Pediat Pneumol Allergol & Neonatol, Biomed Res Endstage & Obstruct Lung Dis Hannover, German Ctr Lung Res, Hannover, Germany Heidelberg Univ, Dept Translat Pulmonol, Translat Lung Res Ctr Heidelberg TLRC, German Ctr Lung Res DZL, Heidelberg, Germany论文数: 引用数: h-index:机构:Gyulumyan, Lena论文数: 0 引用数: 0 h-index: 0机构: Hannover Med Sch, Clin Pediat Pneumol Allergol & Neonatol, Biomed Res Endstage & Obstruct Lung Dis Hannover, German Ctr Lung Res, Hannover, Germany Heidelberg Univ, Dept Translat Pulmonol, Translat Lung Res Ctr Heidelberg TLRC, German Ctr Lung Res DZL, Heidelberg, GermanyScheuermann, Heike论文数: 0 引用数: 0 h-index: 0机构: Heidelberg Univ, Dept Translat Pulmonol, Translat Lung Res Ctr Heidelberg TLRC, German Ctr Lung Res DZL, Heidelberg, Germany Heidelberg Univ, Dept Translat Pulmonol, Translat Lung Res Ctr Heidelberg TLRC, German Ctr Lung Res DZL, Heidelberg, GermanyHirtz, Stephanie论文数: 0 引用数: 0 h-index: 0机构: Heidelberg Univ, Dept Translat Pulmonol, Translat Lung Res Ctr Heidelberg TLRC, German Ctr Lung Res DZL, Heidelberg, Germany Heidelberg Univ, Dept Translat Pulmonol, Translat Lung Res Ctr Heidelberg TLRC, German Ctr Lung Res DZL, Heidelberg, GermanyWege, Sabine论文数: 0 引用数: 0 h-index: 0机构: Univ Hosp Heidelberg, Dept Pneumol & Resp Crit Care Med, Thoraxklin, Heidelberg, Germany Heidelberg Univ, Dept Translat Pulmonol, Translat Lung Res Ctr Heidelberg TLRC, German Ctr Lung Res DZL, Heidelberg, GermanyMairbaeurl, Heimo论文数: 0 引用数: 0 h-index: 0机构: Heidelberg Univ Hosp, Med Clin 7, Sports Med, Heidelberg, Germany Heidelberg Univ, Dept Translat Pulmonol, Translat Lung Res Ctr Heidelberg TLRC, German Ctr Lung Res DZL, Heidelberg, GermanyDorda, Marie论文数: 0 引用数: 0 h-index: 0机构: Hannover Med Sch, Clin Pediat Pneumol Allergol & Neonatol, Biomed Res Endstage & Obstruct Lung Dis Hannover, German Ctr Lung Res, Hannover, Germany Heidelberg Univ, Dept Translat Pulmonol, Translat Lung Res Ctr Heidelberg TLRC, German Ctr Lung Res DZL, Heidelberg, GermanyHyde, Rebecca论文数: 0 引用数: 0 h-index: 0机构: Hannover Med Sch, Clin Pediat Pneumol Allergol & Neonatol, Biomed Res Endstage & Obstruct Lung Dis Hannover, German Ctr Lung Res, Hannover, Germany Heidelberg Univ, Dept Translat Pulmonol, Translat Lung Res Ctr Heidelberg TLRC, German Ctr Lung Res DZL, Heidelberg, GermanyBagheri-Hanson, Azadeh论文数: 0 引用数: 0 h-index: 0机构: Justus Liebig Univ Giessen, UGMLC, Dept Pediat, German Ctr Lung Res DZL, Giessen, Germany Heidelberg Univ, Dept Translat Pulmonol, Translat Lung Res Ctr Heidelberg TLRC, German Ctr Lung Res DZL, Heidelberg, GermanyRueckes-Nilges, Claudia论文数: 0 引用数: 0 h-index: 0机构: Justus Liebig Univ Giessen, UGMLC, Dept Pediat, German Ctr Lung Res DZL, Giessen, Germany Heidelberg Univ, Dept Translat Pulmonol, Translat Lung Res Ctr Heidelberg TLRC, German Ctr Lung Res DZL, Heidelberg, GermanyFischer, Sebastian论文数: 0 引用数: 0 h-index: 0机构: Hannover Med Sch, Clin Pediat Pneumol Allergol & Neonatol, Biomed Res Endstage & Obstruct Lung Dis Hannover, German Ctr Lung Res, Hannover, Germany Heidelberg Univ, Dept Translat Pulmonol, Translat Lung Res Ctr Heidelberg TLRC, German Ctr Lung Res DZL, Heidelberg, GermanyMall, Marcus A.论文数: 0 引用数: 0 h-index: 0机构: Heidelberg Univ, Dept Translat Pulmonol, Translat Lung Res Ctr Heidelberg TLRC, German Ctr Lung Res DZL, Heidelberg, Germany Heidelberg Univ, Dept Translat Pulmonol, Translat Lung Res Ctr Heidelberg TLRC, German Ctr Lung Res DZL, Heidelberg, GermanyTuemmler, Burkhard论文数: 0 引用数: 0 h-index: 0机构: Hannover Med Sch, Clin Pediat Pneumol Allergol & Neonatol, Biomed Res Endstage & Obstruct Lung Dis Hannover, German Ctr Lung Res, Hannover, Germany Heidelberg Univ, Dept Translat Pulmonol, Translat Lung Res Ctr Heidelberg TLRC, German Ctr Lung Res DZL, Heidelberg, Germany
- [22] Lumacaftor/ Ivacaftor improves exercise tolerance in patients with Cystic Fibrosis and severe airflow obstructionBMC Pulmonary Medicine, 19Peter A. B. Wark论文数: 0 引用数: 0 h-index: 0机构: University of Newcastle,Centre for Healthy Lungs, Hunter Medical Research InstituteKim Cookson论文数: 0 引用数: 0 h-index: 0机构: University of Newcastle,Centre for Healthy Lungs, Hunter Medical Research InstituteTheeba Thiruchelvam论文数: 0 引用数: 0 h-index: 0机构: University of Newcastle,Centre for Healthy Lungs, Hunter Medical Research InstituteJohn Brannan论文数: 0 引用数: 0 h-index: 0机构: University of Newcastle,Centre for Healthy Lungs, Hunter Medical Research InstituteDouglas J. Dorahy论文数: 0 引用数: 0 h-index: 0机构: University of Newcastle,Centre for Healthy Lungs, Hunter Medical Research Institute
- [23] Safety and efficacy of treatment with lumacaftor in combination with ivacaftor in younger patients with cystic fibrosisEXPERT REVIEW OF RESPIRATORY MEDICINE, 2019, 13 (05) : 417 - 423Cheng, Pi Chun论文数: 0 引用数: 0 h-index: 0机构: Childrens Hosp Philadelphia, Div Pulm Med, Philadelphia, PA 19104 USA Childrens Hosp Philadelphia, Cyst Fibrosis Ctr, Abramson Res Ctr Room 410A,3615 Civ Ctr Blvd, Philadelphia, PA 19104 USA Childrens Hosp Philadelphia, Div Pulm Med, Philadelphia, PA 19104 USAAlexiou, Stamatia论文数: 0 引用数: 0 h-index: 0机构: Childrens Hosp Philadelphia, Div Pulm Med, Philadelphia, PA 19104 USA Childrens Hosp Philadelphia, Cyst Fibrosis Ctr, Abramson Res Ctr Room 410A,3615 Civ Ctr Blvd, Philadelphia, PA 19104 USA Childrens Hosp Philadelphia, Div Pulm Med, Philadelphia, PA 19104 USARubenstein, Ronald C.论文数: 0 引用数: 0 h-index: 0机构: Childrens Hosp Philadelphia, Div Pulm Med, Philadelphia, PA 19104 USA Childrens Hosp Philadelphia, Cyst Fibrosis Ctr, Abramson Res Ctr Room 410A,3615 Civ Ctr Blvd, Philadelphia, PA 19104 USA Childrens Hosp Philadelphia, Div Pulm Med, Philadelphia, PA 19104 USA
- [24] EFFECTS OF LUMACAFTOR-IVACAFTOR THERAPY ON CFTR FUNCTION IN PHE508DEL HOMOZYGOUS PATIENTS WITH CYSTIC FIBROSISPEDIATRIC PULMONOLOGY, 2018, 53 : 235 - 235Graeber, S. Y.论文数: 0 引用数: 0 h-index: 0机构: Charite Univ Med Berlin, Dept Pediat Pulmonol Immunol & Intens Care Med, Berlin, Germany Heidelberg Univ, Dept Translat Pulmonol, Translat Lung Res Ctr Heidelberg TLRC, German Ctr Lung Res DZL, Heidelberg, Germany Heidelberg Univ, Div Pediat Pulmonol & Allergy, Heidelberg, Germany Heidelberg Univ, Cyst Fibrosis Ctr, Dept Pediat, Heidelberg, Germany Charite Univ Med Berlin, Dept Pediat Pulmonol Immunol & Intens Care Med, Berlin, GermanyDopfer, C.论文数: 0 引用数: 0 h-index: 0机构: Hannover Med Sch, Clin Pediat Pneumol Allergol & Neonatol, Hannover, Germany Hannover Med Sch, Biomed Res Endstage & Obstruct Lung Dis Hannover, German Ctr Lung Res, Hannover, Germany Charite Univ Med Berlin, Dept Pediat Pulmonol Immunol & Intens Care Med, Berlin, Germany论文数: 引用数: h-index:机构:Gyulumyan, L.论文数: 0 引用数: 0 h-index: 0机构: Hannover Med Sch, Clin Pediat Pneumol Allergol & Neonatol, Hannover, Germany Charite Univ Med Berlin, Dept Pediat Pulmonol Immunol & Intens Care Med, Berlin, GermanyScheuermann, H.论文数: 0 引用数: 0 h-index: 0机构: Heidelberg Univ, Dept Translat Pulmonol, Translat Lung Res Ctr Heidelberg TLRC, German Ctr Lung Res DZL, Heidelberg, Germany Charite Univ Med Berlin, Dept Pediat Pulmonol Immunol & Intens Care Med, Berlin, GermanyHirtz, S.论文数: 0 引用数: 0 h-index: 0机构: Heidelberg Univ, Dept Translat Pulmonol, Translat Lung Res Ctr Heidelberg TLRC, German Ctr Lung Res DZL, Heidelberg, Germany Charite Univ Med Berlin, Dept Pediat Pulmonol Immunol & Intens Care Med, Berlin, GermanyWege, S.论文数: 0 引用数: 0 h-index: 0机构: Univ Hosp Heidelberg, Dept Pneumol & Resp Crit Care Med, Thoraxklin, Heidelberg, Germany Charite Univ Med Berlin, Dept Pediat Pulmonol Immunol & Intens Care Med, Berlin, GermanyMairbaeurl, H.论文数: 0 引用数: 0 h-index: 0机构: Heidelberg Univ Hosp, Med Clin 7, Sports Med, Heidelberg, Germany Charite Univ Med Berlin, Dept Pediat Pulmonol Immunol & Intens Care Med, Berlin, GermanyDorda, M.论文数: 0 引用数: 0 h-index: 0机构: Hannover Med Sch, Clin Pediat Pneumol Allergol & Neonatol, Hannover, Germany Charite Univ Med Berlin, Dept Pediat Pulmonol Immunol & Intens Care Med, Berlin, GermanyHyde, R.论文数: 0 引用数: 0 h-index: 0机构: Hannover Med Sch, Clin Pediat Pneumol Allergol & Neonatol, Hannover, Germany Hannover Med Sch, Biomed Res Endstage & Obstruct Lung Dis Hannover, German Ctr Lung Res, Hannover, Germany Charite Univ Med Berlin, Dept Pediat Pulmonol Immunol & Intens Care Med, Berlin, GermanyBagheri-Hanson, A.论文数: 0 引用数: 0 h-index: 0机构: Justus Liebig Univ Giessen, Dept Pediat, Giessen, Germany Charite Univ Med Berlin, Dept Pediat Pulmonol Immunol & Intens Care Med, Berlin, GermanyRueckes-Nilges, C.论文数: 0 引用数: 0 h-index: 0机构: Justus Liebig Univ Giessen, Dept Pediat, Giessen, Germany UGMLC, German Ctr Lung Res DZI, Giessen, Germany Charite Univ Med Berlin, Dept Pediat Pulmonol Immunol & Intens Care Med, Berlin, GermanyFischer, S.论文数: 0 引用数: 0 h-index: 0机构: Hannover Med Sch, Clin Pediat Pneumol Allergol & Neonatol, Hannover, Germany Hannover Med Sch, Biomed Res Endstage & Obstruct Lung Dis Hannover, German Ctr Lung Res, Hannover, Germany Charite Univ Med Berlin, Dept Pediat Pulmonol Immunol & Intens Care Med, Berlin, GermanyMall, M. A.论文数: 0 引用数: 0 h-index: 0机构: Charite Univ Med Berlin, Dept Pediat Pulmonol Immunol & Intens Care Med, Berlin, Germany Heidelberg Univ, Dept Translat Pulmonol, Translat Lung Res Ctr Heidelberg TLRC, German Ctr Lung Res DZL, Heidelberg, Germany Heidelberg Univ, Div Pediat Pulmonol & Allergy, Heidelberg, Germany Heidelberg Univ, Cyst Fibrosis Ctr, Dept Pediat, Heidelberg, Germany Charite Univ Med Berlin, Dept Pediat Pulmonol Immunol & Intens Care Med, Berlin, GermanyTummler, B.论文数: 0 引用数: 0 h-index: 0机构: Hannover Med Sch, Clin Pediat Pneumol Allergol & Neonatol, Hannover, Germany Hannover Med Sch, Biomed Res Endstage & Obstruct Lung Dis Hannover, German Ctr Lung Res, Hannover, Germany Charite Univ Med Berlin, Dept Pediat Pulmonol Immunol & Intens Care Med, Berlin, Germany
- [25] Effects of Lumacaftor-Ivacaftor Therapy on Cystic Fibrosis Transmembrane Conductance Regulator Function in Phe508del Homozygous Patients with Cystic FibrosisAMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2018, 197 (11) : 1433 - 1442Graeber, Simon Y.论文数: 0 引用数: 0 h-index: 0机构: Heidelberg Univ, German Ctr Lung Res, Dept Translat Pulmonol, Heidelberg, Germany Heidelberg Univ, German Ctr Lung Res, Div Pediat Pulmonol & Allergy, Heidelberg, Germany Heidelberg Univ, German Ctr Lung Res, Cyst Fibrosis Ctr, Dept Pediat, Heidelberg, Germany Heidelberg Univ, German Ctr Lung Res, Translat Lung Res Ctr Heidelberg, Heidelberg, Germany Charite Univ Med Berlin, Dept Pediat Pulmonol & Immunol, Berlin, Germany Charite Univ Med Berlin, Cyst Fibrosis Ctr, Berlin, Germany Heidelberg Univ, German Ctr Lung Res, Dept Translat Pulmonol, Heidelberg, GermanyDopfer, Christian论文数: 0 引用数: 0 h-index: 0机构: Hannover Med Sch, German Ctr Lung Res, Clin Pediat Pneumol Allergol & Neonatol, Hannover, Germany Hannover Med Sch, German Ctr Lung Res, Biomed Res Endstage & Obstruct Lung Dis Hannover, Hannover, Germany Heidelberg Univ, German Ctr Lung Res, Dept Translat Pulmonol, Heidelberg, Germany论文数: 引用数: h-index:机构:Gyulumyan, Lena论文数: 0 引用数: 0 h-index: 0机构: Hannover Med Sch, German Ctr Lung Res, Clin Pediat Pneumol Allergol & Neonatol, Hannover, Germany Heidelberg Univ, German Ctr Lung Res, Dept Translat Pulmonol, Heidelberg, GermanyScheuermann, Heike论文数: 0 引用数: 0 h-index: 0机构: Heidelberg Univ, German Ctr Lung Res, Dept Translat Pulmonol, Heidelberg, Germany Heidelberg Univ, German Ctr Lung Res, Dept Translat Pulmonol, Heidelberg, GermanyHirtz, Stephanie论文数: 0 引用数: 0 h-index: 0机构: Heidelberg Univ, German Ctr Lung Res, Dept Translat Pulmonol, Heidelberg, Germany Heidelberg Univ, German Ctr Lung Res, Dept Translat Pulmonol, Heidelberg, GermanyWege, Sabine论文数: 0 引用数: 0 h-index: 0机构: Univ Hosp Heidelberg, Thoraxklin, Dept Pneumol & Resp Crit Care Med, Heidelberg, Germany Heidelberg Univ, German Ctr Lung Res, Dept Translat Pulmonol, Heidelberg, GermanyMairbaeurl, Heimo论文数: 0 引用数: 0 h-index: 0机构: Heidelberg Univ, German Ctr Lung Res, Translat Lung Res Ctr Heidelberg, Heidelberg, Germany Univ Hosp Heidelberg, Thoraxklin, Dept Pneumol & Resp Crit Care Med, Heidelberg, Germany Heidelberg Univ Hosp, Sports Med, Med Clin 7, Heidelberg, Germany Heidelberg Univ, German Ctr Lung Res, Dept Translat Pulmonol, Heidelberg, GermanyDorda, Marie论文数: 0 引用数: 0 h-index: 0机构: Hannover Med Sch, German Ctr Lung Res, Clin Pediat Pneumol Allergol & Neonatol, Hannover, Germany Hannover Med Sch, German Ctr Lung Res, Biomed Res Endstage & Obstruct Lung Dis Hannover, Hannover, Germany Heidelberg Univ, German Ctr Lung Res, Dept Translat Pulmonol, Heidelberg, GermanyHyde, Rebecca论文数: 0 引用数: 0 h-index: 0机构: Hannover Med Sch, German Ctr Lung Res, Clin Pediat Pneumol Allergol & Neonatol, Hannover, Germany Hannover Med Sch, German Ctr Lung Res, Biomed Res Endstage & Obstruct Lung Dis Hannover, Hannover, Germany Heidelberg Univ, German Ctr Lung Res, Dept Translat Pulmonol, Heidelberg, GermanyBagheri-Hanson, Azadeh论文数: 0 引用数: 0 h-index: 0机构: Justus Liebig Univ Giessen, Dept Pediat, Giessen, Germany Heidelberg Univ, German Ctr Lung Res, Dept Translat Pulmonol, Heidelberg, GermanyRueckes-Nilges, Claudia论文数: 0 引用数: 0 h-index: 0机构: Justus Liebig Univ Giessen, Dept Pediat, Giessen, Germany Univ Giessen, Giessen, Germany German Ctr Lung Res, Marburg Lung Ctr, Giessen, Germany Heidelberg Univ, German Ctr Lung Res, Dept Translat Pulmonol, Heidelberg, GermanyFischer, Sebastian论文数: 0 引用数: 0 h-index: 0机构: Hannover Med Sch, German Ctr Lung Res, Clin Pediat Pneumol Allergol & Neonatol, Hannover, Germany Hannover Med Sch, German Ctr Lung Res, Biomed Res Endstage & Obstruct Lung Dis Hannover, Hannover, Germany Heidelberg Univ, German Ctr Lung Res, Dept Translat Pulmonol, Heidelberg, GermanyMall, Marcus A.论文数: 0 引用数: 0 h-index: 0机构: Heidelberg Univ, German Ctr Lung Res, Dept Translat Pulmonol, Heidelberg, Germany Heidelberg Univ, German Ctr Lung Res, Div Pediat Pulmonol & Allergy, Heidelberg, Germany Heidelberg Univ, German Ctr Lung Res, Cyst Fibrosis Ctr, Dept Pediat, Heidelberg, Germany Heidelberg Univ, German Ctr Lung Res, Translat Lung Res Ctr Heidelberg, Heidelberg, Germany Charite Univ Med Berlin, Dept Pediat Pulmonol & Immunol, Berlin, Germany Charite Univ Med Berlin, Cyst Fibrosis Ctr, Berlin, Germany Heidelberg Univ, German Ctr Lung Res, Dept Translat Pulmonol, Heidelberg, GermanyTuemmler, Burkhard论文数: 0 引用数: 0 h-index: 0机构: Hannover Med Sch, German Ctr Lung Res, Clin Pediat Pneumol Allergol & Neonatol, Hannover, Germany Hannover Med Sch, German Ctr Lung Res, Biomed Res Endstage & Obstruct Lung Dis Hannover, Hannover, Germany Heidelberg Univ, German Ctr Lung Res, Dept Translat Pulmonol, Heidelberg, Germany
- [26] Patients with cystic fibrosis and advanced lung disease benefit from lumacaftor/ivacaftor treatmentPEDIATRIC PULMONOLOGY, 2020, 55 (12) : 3364 - 3370Ejiofor, Linnea Chika Kristensen论文数: 0 引用数: 0 h-index: 0机构: Copenhagen Univ Hosp, Rigshosp, Dept Infect Dis, Esther Moellers Vej 6,Opgang 86,3 Sal, DK-2100 Copenhagen, Denmark Copenhagen Univ Hosp, Rigshosp, Dept Infect Dis, Esther Moellers Vej 6,Opgang 86,3 Sal, DK-2100 Copenhagen, DenmarkMathiesen, Inger Hee Mabuza论文数: 0 引用数: 0 h-index: 0机构: Copenhagen Univ Hosp, Rigshosp, Dept Infect Dis, Esther Moellers Vej 6,Opgang 86,3 Sal, DK-2100 Copenhagen, Denmark Copenhagen Univ Hosp, Rigshosp, Dept Infect Dis, Esther Moellers Vej 6,Opgang 86,3 Sal, DK-2100 Copenhagen, DenmarkJensen-Fangel, Soren论文数: 0 引用数: 0 h-index: 0机构: Aarhus Univ Hosp, Dept Infect Dis, Aarhus N, Denmark Copenhagen Univ Hosp, Rigshosp, Dept Infect Dis, Esther Moellers Vej 6,Opgang 86,3 Sal, DK-2100 Copenhagen, DenmarkOlesen, Hanne Vebert论文数: 0 引用数: 0 h-index: 0机构: Aarhus Univ Hosp, Dept Children & Adolescent Med, Aarhus N, Denmark Copenhagen Univ Hosp, Rigshosp, Dept Infect Dis, Esther Moellers Vej 6,Opgang 86,3 Sal, DK-2100 Copenhagen, DenmarkSkov, Marianne论文数: 0 引用数: 0 h-index: 0机构: Copenhagen Univ Hosp, Rigshosp, Dept Pediat & Adolescent Med, Copenhagen, Denmark Copenhagen Univ Hosp, Rigshosp, Dept Infect Dis, Esther Moellers Vej 6,Opgang 86,3 Sal, DK-2100 Copenhagen, DenmarkPhilipsen, Lue Katrine Drasbaek论文数: 0 引用数: 0 h-index: 0机构: Copenhagen Univ Hosp, Rigshosp, Cyst Fibrosis Ctr, Copenhagen, Denmark Copenhagen Univ Hosp, Rigshosp, Dept Infect Dis, Esther Moellers Vej 6,Opgang 86,3 Sal, DK-2100 Copenhagen, DenmarkPedersen, Camilla Lundgren论文数: 0 引用数: 0 h-index: 0机构: Aarhus Univ Hosp, Dept Physiotherapy & Occupat Therapy, Aarhus N, Denmark Copenhagen Univ Hosp, Rigshosp, Dept Infect Dis, Esther Moellers Vej 6,Opgang 86,3 Sal, DK-2100 Copenhagen, DenmarkPressler, Tacjana论文数: 0 引用数: 0 h-index: 0机构: Copenhagen Univ Hosp, Rigshosp, Cyst Fibrosis Ctr, Copenhagen, Denmark Copenhagen Univ Hosp, Rigshosp, Dept Infect Dis, Esther Moellers Vej 6,Opgang 86,3 Sal, DK-2100 Copenhagen, Denmark
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