A case of parietal meningoencephalocele associated with multiple intracranial anomalies

Parietal cephaloceles are rare congenital anomalies usually associated with significant underlying brain anomalies. Further investigations with cranial magnetic resonance examination and MR venography is important to reveal associated intracranial anomalies and to show the relationship of the cephalocele sac with the dural venous sinuses. These examinations are also crucial to predict the prognosis before surgical correction of the encephalocele. We present, MR findings of an infant with a parietal meningoencephalocele associated with microcephaly and multiple other congenital central nervous system anomalies including partial callosal agenesis, gray matter heterotopia, ventricular dysplasia, and right retrocerebellar arachnoid cyst.