Supravalvular stenotic mitral ring with ventricular septal defect

Background: Supravalvular mitral ring is exceedingly uncommon, Methods: We report a 4-year-old girl with supravalvular stenotic mitral ring and ventricular septal defect (VSD), The VSD was closed by a Dacron patch and the supravalvular ring was excised, For treatment of supravalvular mitral ring with obstruction, surgical resection is commonly performed, Results: There are no reports of long-term follow-up after resecting the supravalvular mitral ring, Conclusion: In our case, no mitral stenosis was evident on postoperative echocardiogram performed 3 years after surgery.