Congenital absence of portal vein associated with nodular regenerative hyperplasia of the liver and pulmonary hypertension

被引：12
|
作者：
Peker, Ahmet [1 ]
Ucar, Tayfun [2 ]
Kuloglu, Zarife [2 ]
Ceyhan, Koray [3 ]
Tutar, Ercan [2 ]
Fitoz, Suat [1 ]
机构：
[1] Ankara Univ, Sch Med, Dept Radiol, TR-06100 Ankara, Turkey
[2] Ankara Univ, Sch Med, Dept Pediat, TR-06100 Ankara, Turkey
[3] Ankara Univ, Sch Med, Dept Pathol, TR-06100 Ankara, Turkey
来源：
CLINICAL IMAGING | 2009年 / 33卷 / 04期
关键词：
Portal vein; Congenital absence; Computed tomography; Ultrasonography; Magnetic resonance imaging; HEPATOPULMONARY SYNDROME;
D O I：
10.1016/j.clinimag.2008.12.011
中图分类号：
R8 [特种医学]; R445 [影像诊断学];
学科分类号：
1002 ; 100207 ; 1009 ;
摘要：
We present a 15-year-old girl with congenital absence of the portal vein, pulmonary arterial hypertension and multiple liver lesions proven to be nodular regenerative hyperplasia with biopsy. Ultrasonography, computed tomography, and magnetic resonance imaging findings of the liver lesions and Type I portosystemic shunt are presented. (C) 2009 Elsevier Inc. All rights reserved.
引用
收藏
页码：322 / 325
页数：4
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