Orbital tumour as initial manifestation of acute myeloid leukemia:: Granulocytic sarcoma:: Case report

被引:13
|
作者
Maka, Erika [1 ]
Lukats, Olga [1 ]
Toth, Jeannette [1 ]
Fekete, Sandor [2 ]
机构
[1] Semmelweis Univ, Dept Ophthalmol, Fac Med, H-1083 Budapest, Hungary
[2] Szent Laszlo Hosp, Div Haematol, Budapest, Hungary
关键词
orbital granulocytic sarcoma; acute myeloid leukemia;
D O I
10.1007/s12253-008-9028-x
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
We report orbital involvement as an initial manifestation of acute myeloid leukemia in a 57-year-old woman. The patient presented with painful proptosis and limited ocular motility. Orbital computed tomography revealed bilateral homogeneous masses. Orbital biopsy was performed on the right side; and histopathology disclosed a myelocytic tumour. Despite treatment using irradiation and chemotherapy, the patient died eleven months after presentation. There appear to be only a few previous reports of acute myeloid leukemia cases presenting with orbital involvement, and most cases occurred in children. This very rare condition has a poor survival prognosis, even with radiation treatment and chemotherapy.
引用
收藏
页码:209 / 211
页数:3
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