Clinical response to sildenafil in pulmonary hypertension associated with Gaucher disease

被引:8
|
作者
Fernandes, CJC
Jardim, C
Carvalho, LAS
Farias, AQ
Terra, M
Souza, R
机构
[1] Univ Sao Paulo, Sch Med, Div Pulm, Pulm Hypertens Unit, Sao Paulo, Brazil
[2] Univ Sao Paulo, Sch Med, Div Gastroenterol, Sao Paulo, Brazil
关键词
D O I
10.1007/s10545-005-0603-y
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
There are few reports of pulmonary hypertension in Gaucher disease. We report a patient who showed significant clinical improvement after treatment with sildenafil.
引用
收藏
页码:603 / 605
页数:3
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