Haemophagocytic syndrome (HPS) results from an inappropriate stimulation of macrophages in bone marrow and lymphoid organs, leading to haemophagocytosis and hypercytokinemia. HPS may be primitive, essentially in pediatric population, or secondary to malignancy, infection or autoimmune disease. This disease is rare and prognosis is poor. A small number of cases during pregnancy have been described in literature. We report one HPS case in a pregnant patient at 21 week's gestation with systemic lupus erythematosus. We discuss diagnostic difficulties, obstetrical complications and therapeutic options. (C) 2011 Societe francaise d'anesthesie et de reanimation (Sfar). Published by Elsevier Masson SAS. All rights reserved.
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Zekai Tahir Burak Womens Hlth Educ & Res Hosp, High Risk Pregnancy Clin, Ankara, TurkeyZekai Tahir Burak Womens Hlth Educ & Res Hosp, High Risk Pregnancy Clin, Ankara, Turkey
Keskin, HL
Mungan, T
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Zekai Tahir Burak Womens Hlth Educ & Res Hosp, High Risk Pregnancy Clin, Ankara, TurkeyZekai Tahir Burak Womens Hlth Educ & Res Hosp, High Risk Pregnancy Clin, Ankara, Turkey
Mungan, T
Aktepe-Keskin, E
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Zekai Tahir Burak Womens Hlth Educ & Res Hosp, High Risk Pregnancy Clin, Ankara, TurkeyZekai Tahir Burak Womens Hlth Educ & Res Hosp, High Risk Pregnancy Clin, Ankara, Turkey
Aktepe-Keskin, E
Güngör, T
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Zekai Tahir Burak Womens Hlth Educ & Res Hosp, High Risk Pregnancy Clin, Ankara, TurkeyZekai Tahir Burak Womens Hlth Educ & Res Hosp, High Risk Pregnancy Clin, Ankara, Turkey