We report pyoderma gangrenosum in two siblings with onset during childhood and no associated systemic abnormalities. The patients were born of nonconsanguineous, healthy parents. Treatment with oral corticosteroids produced an excellent clinical response, followed by recurrence after cessation of therapy. Steroids were restarted in combination with dapsone to prevent further recurrence.
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Grp Hosp Bichat Claude Bernard, Dermatol Serv, AP HP, F-75018 Paris, FranceGrp Hosp Bichat Claude Bernard, Dermatol Serv, AP HP, F-75018 Paris, France
Mahé, E
Descamps, V
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Grp Hosp Bichat Claude Bernard, Dermatol Serv, AP HP, F-75018 Paris, FranceGrp Hosp Bichat Claude Bernard, Dermatol Serv, AP HP, F-75018 Paris, France
Descamps, V
Belaïch, S
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Grp Hosp Bichat Claude Bernard, Dermatol Serv, AP HP, F-75018 Paris, FranceGrp Hosp Bichat Claude Bernard, Dermatol Serv, AP HP, F-75018 Paris, France
Belaïch, S
Cricks, B
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Grp Hosp Bichat Claude Bernard, Dermatol Serv, AP HP, F-75018 Paris, FranceGrp Hosp Bichat Claude Bernard, Dermatol Serv, AP HP, F-75018 Paris, France
机构:
Univ S Florida, Coll Med, H Lee Moffitt Canc Ctr & Res Inst, Tampa, FL 33612 USAUniv S Florida, Coll Med, H Lee Moffitt Canc Ctr & Res Inst, Tampa, FL 33612 USA
Coleman, EN
Greene, JN
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Univ S Florida, Coll Med, H Lee Moffitt Canc Ctr & Res Inst, Tampa, FL 33612 USAUniv S Florida, Coll Med, H Lee Moffitt Canc Ctr & Res Inst, Tampa, FL 33612 USA