A rare cause of intracranial hemorrhage:: Factor X deficiency

被引:13
|
作者
Çitak, A [1 ]
Üçsel, R [1 ]
Karaböcüoglu, M [1 ]
Ünüvar, A [1 ]
Uzel, N [1 ]
机构
[1] Istanbul Univ, Inst Child Hlth, Dept Pediat Emergency, Istanbul, Turkey
关键词
Factor X deficiency; intracranial hemorrhage;
D O I
10.1097/00006565-200110000-00007
中图分类号
R4 [临床医学];
学科分类号
1002 ; 100602 ;
摘要
Congenital factor X deficiency is a rare inherited coagulation disorder, characterized by prolonged prothrombin time and partial thromboplastin time. For the definite diagnosis, specific factor X level should be investigated. We describe a patient with factor X deficiency who had intracranial hemorrhage. Hematologic tests showed prolonged prothrombin time, partial thromboplastin time, and a factor X level of 5%. The patient's hemorrhage resolved with fresh frozen plasma replacement. In this article, we discuss the clinical features and management of factor X deficiency.
引用
收藏
页码:349 / 350
页数:2
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