A rare cause of intracranial hemorrhage:: Factor X deficiency

被引:13
|
作者
Çitak, A [1 ]
Üçsel, R [1 ]
Karaböcüoglu, M [1 ]
Ünüvar, A [1 ]
Uzel, N [1 ]
机构
[1] Istanbul Univ, Inst Child Hlth, Dept Pediat Emergency, Istanbul, Turkey
关键词
Factor X deficiency; intracranial hemorrhage;
D O I
10.1097/00006565-200110000-00007
中图分类号
R4 [临床医学];
学科分类号
1002 ; 100602 ;
摘要
Congenital factor X deficiency is a rare inherited coagulation disorder, characterized by prolonged prothrombin time and partial thromboplastin time. For the definite diagnosis, specific factor X level should be investigated. We describe a patient with factor X deficiency who had intracranial hemorrhage. Hematologic tests showed prolonged prothrombin time, partial thromboplastin time, and a factor X level of 5%. The patient's hemorrhage resolved with fresh frozen plasma replacement. In this article, we discuss the clinical features and management of factor X deficiency.
引用
收藏
页码:349 / 350
页数:2
相关论文
共 50 条
  • [1] FACTOR-X DEFICIENCY - A RARE CAUSE OF SCROTAL HEMORRHAGE
    RUANE, BJ
    MCCORD, FB
    IRISH MEDICAL JOURNAL, 1990, 83 (04) : 163 - 163
  • [2] SEVERE CONGENITAL FACTOR-X DEFICIENCY WITH INTRACRANIAL HEMORRHAGE
    SUMER, T
    AHMAD, M
    SUMER, NK
    ALMOUZAN, MI
    EUROPEAN JOURNAL OF PEDIATRICS, 1986, 145 (1-2) : 119 - 120
  • [3] Factor X Deficiency: A Rare Cause of Puberty Menorrhagia
    Virender Singh
    Tania Kakkar
    Sanjeev K. Digra
    Manisha Kakkar
    The Indian Journal of Pediatrics, 2013, 80 : 607 - 608
  • [4] Factor X Deficiency: A Rare Cause of Puberty Menorrhagia
    Singh, Virender
    Kakkar, Tania
    Digra, Sanjeev K.
    Kakkar, Manisha
    INDIAN JOURNAL OF PEDIATRICS, 2013, 80 (07): : 607 - 608
  • [5] Intracranial hemorrhage in factor XIII deficiency
    Naderi, M.
    Eshghi, P.
    Karimi, M.
    Dorgalaleh, A.
    Tabibian, S.
    JOURNAL OF THROMBOSIS AND HAEMOSTASIS, 2013, 11 : 809 - 810
  • [6] FACTOR XIII DEFICIENCY WITH INTRACRANIAL HEMORRHAGE
    Mirbehbahani, N. B.
    HAEMATOLOGICA, 2015, 100 : 673 - 674
  • [7] RUPTURED INTRACRANIAL MYCOTIC-ANEURYSM - A RARE CAUSE OF INTRACRANIAL HEMORRHAGE
    KONG, KH
    CHAN, KF
    ARCHIVES OF PHYSICAL MEDICINE AND REHABILITATION, 1995, 76 (03): : 287 - 289
  • [8] Factor VII deficiency revealed by intracranial hemorrhage
    Ben Mansour, L. Sfaihi
    Thabet, A.
    Aloulou, H.
    Turki, H.
    Chabchoub, I.
    Mhiri, F.
    Mnif, Z.
    Ben Ali, H.
    Kammoun, T.
    Hachicha, M.
    ARCHIVES DE PEDIATRIE, 2009, 16 (07): : 1024 - 1027
  • [9] Congenital coagulation factor V deficiency with intracranial hemorrhage
    Yang, Jingjing
    Mao, Hongli
    Sun, Li
    JOURNAL OF CLINICAL LABORATORY ANALYSIS, 2022, 36 (11)
  • [10] INTRACRANIAL HEMORRHAGE IN CONGENITAL DEFICIENCY OF FACTOR-XIII
    ABBONDANZO, SL
    GOOTENBERG, JE
    LOFTS, RS
    MCPHERSON, RA
    AMERICAN JOURNAL OF PEDIATRIC HEMATOLOGY ONCOLOGY, 1988, 10 (01): : 65 - 68