Congenital insensitivity to pain: Orthopaedic implications

被引:11
|
作者
Kuo, RS [1 ]
Macnicol, MF [1 ]
机构
[1] PRINCESS MARGARET ROSE ORTHOPAED HOSP, EDINBURGH EH10 7ED, MIDLOTHIAN, SCOTLAND
来源
关键词
pain insensitivity; mental retardation; osteomyelitis; Charcot; neuropathic;
D O I
10.1097/01202412-199605040-00013
中图分类号
R826.8 [整形外科学]; R782.2 [口腔颌面部整形外科学]; R726.2 [小儿整形外科学]; R62 [整形外科学(修复外科学)];
学科分类号
摘要
We report two children in one family with congenital insensitivity to pain, anhidrosis, and mental retardation with behavioural disturbance. Orthopaedic manifestations of this condition include recurrent fractures, osteomyelitis, and neuropathic joints. The differential diagnoses and difficulties in the management of this rare disorder are discussed.
引用
收藏
页码:292 / 295
页数:4
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