Hybrid procedure as a palliation approach in truncus arteriosus with interrupted aortic arch

被引:0
|
作者
Mohsin, Muhammad [1 ]
Ahmed, Waris [1 ]
Karim, Farida [1 ]
Sadqani, Saleem Akhtar [1 ]
机构
[1] Aga Khan Univ Hosp, Dept Pediat, Karachi, Pakistan
关键词
Truncus arteriosus; Hybrid procedure; PDA stenting; REPAIR; MANAGEMENT; SURGERY;
D O I
10.1016/j.ppedcard.2019.101174
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Truncus arteriosus with interrupted aortic arch (Van Pragh A4) is a rare cyanotic heart disease. The management of this clinical entity is challenging due to obstructed systemic circulation, which required early intervention, especially in clinical setting with limited resources. Complete repair in early neonatal period associated with high morbidity and mortality. We present two patients with truncus arteriosus (type A4) palliated with hybrid procedure previously reported for management of patients with hypoplastic left heart syndrome.
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页数:4
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