Malignant peripheral nerve sheath tumor - The clinical spectrum and outcome of treatment

被引:113
|
作者
Baehring, JM
Betensky, RA
Batchelor, TT
机构
[1] Harvard Univ, Massachusetts Gen Hosp, Sch Med, Brain Tumor Ctr,Dept Neurol, Boston, MA 02114 USA
[2] Harvard Univ, Sch Publ Hlth, Dept Biostat, Boston, MA 02115 USA
关键词
D O I
10.1212/01.WNL.0000078813.05925.2C
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Malignant peripheral nerve sheath tumors (MPNST) are derived from Schwann cells or pluripotent cells of the neural crest. Delay of diagnosis is common, especially in lesions affecting proximal parts of the peripheral nervous system. Presented is a series of 54 patients with MPNST seen at a single institution over a 10-year period. In this series, tumor diameter of <5 cm, gross total resection of the tumor, and younger age were favorable prognostic variables.
引用
收藏
页码:696 / 698
页数:3
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