Bullous systemic lupus erythematosus in a 10-year-old child

被引:4
|
作者
Hans-Bittner, Nelise Ritter [1 ]
Bittner, Guilherme Canho [1 ]
Hans Filho, Gunter [1 ,2 ]
Takita, Luiz Carlos [1 ,3 ]
机构
[1] Univ Fed Mato Grosso Sul HUMAP UFMS, Dr Gunter Hans Dept Dermatol, Hosp Univ Maria Aparecida Pedrossian, Campo Grande, MS, Brazil
[2] Univ Fed Mato Grosso Sul FAMED UFMS, Fac Med, Discipline Dermatol, Campo Grande, MS, Brazil
[3] Univ Fed Mato Grosso Sul FAMED UFMS, Fac Med, Discipline Pathol, Campo Grande, MS, Brazil
关键词
Autoimmunity; Skin diseases; vesiculobullous; Lupus erythematosus; systemic; DIAGNOSIS;
D O I
10.1590/abd1806-4841.20176074
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Bullous systemic lupus erythematosus (BSLE) is a rare autoimmune subepidermal blistering disease, with few cases described in childhood. It has different clinical-pathological features. We report a case of BSLE in a 10-year-old child with systemic lupus erythematosus, treated with prednisone and hydroxychloroquine. There was complete remission with dapsone, with no recurrence of skin lesions throughout one year of follow-up. We highlight the rarity and early age of occurrence.
引用
收藏
页码:37 / 39
页数:3
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