Intrapericardial teratoma with hydrops leading to in utero demise

被引:13
|
作者
Pachy, F.
Raiffort, C.
Mechler, C.
Zilberman, S.
Mandelbrot, L.
机构
[1] Hop Louis Mourier, Dept Pathol, F-92701 Colombes, France
[2] Univ Paris 07, F-75221 Paris 05, France
关键词
intra-pericardial teratoma; nonimmune hydrops; prenatal diagnosis;
D O I
10.1002/pd.1798
中图分类号
Q3 [遗传学];
学科分类号
071007 ; 090102 ;
摘要
We report a case of intrapericardial teratoma following in utero demise at 29 weeks with nonimmune hydrops. The diagnosis was strongly suggested by ultrasound findings and confirmed by fetopathology. The mechanism whereby intrapericardial teratomas may lead to hydrops and death is massive pericardial effusion responsible for compressive tamponade. When prenatal diagnosis is performed before this stage, in utero interventions can obtain decompression, and the birth can be planned with rapid and appropriate management of the neonate. Copyright (C) 2007 John Wiley & Sons, Ltd.
引用
收藏
页码:970 / 972
页数:3
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