Porokeratosis is a group of hereditary or acquired disorders of epidermal keratinization, characterized by keratotic lesions with an atrophic center and a prominent peripheral ridge. At least seven clinical variants have been identified: the plaque type, disseminated superficial porokeratosis, disseminated superficial actinic porokeratosis, linear porokeratosis, giant porokeratosis, porokeratosis plantaris palmaris et disseminate, and punctuate porokeratosis. Genital porokeratosis is a rare condition even in disseminated forms. We described two male patients who had porokeratosis only affecting the scrotum. The patients were treated by surgical excision under local anesthesia. One-year follow-up revealed no sign of recurrences and malignant changes.
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Univ Sao Paulo, Fac Med, Div Rheumatol & Radiol, Pediat Rheumatol Unit, Sao Paulo, BrazilUniv Sao Paulo, Fac Med, Div Rheumatol & Radiol, Pediat Rheumatol Unit, Sao Paulo, Brazil
Sallum, A. M. E.
Garcia, A. J. M.
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Univ Sao Paulo, Fac Med, Div Rheumatol & Radiol, Pediat Rheumatol Unit, Sao Paulo, BrazilUniv Sao Paulo, Fac Med, Div Rheumatol & Radiol, Pediat Rheumatol Unit, Sao Paulo, Brazil
Garcia, A. J. M.
Saito, O. C.
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Univ Sao Paulo, Fac Med, Div Rheumatol & Radiol, Pediat Rheumatol Unit, Sao Paulo, BrazilUniv Sao Paulo, Fac Med, Div Rheumatol & Radiol, Pediat Rheumatol Unit, Sao Paulo, Brazil
Saito, O. C.
Silva, C. A. A.
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Univ Sao Paulo, Fac Med, Div Rheumatol & Radiol, Pediat Rheumatol Unit, Sao Paulo, BrazilUniv Sao Paulo, Fac Med, Div Rheumatol & Radiol, Pediat Rheumatol Unit, Sao Paulo, Brazil