Diagnosing and managing scleroderma-related pulmonary arterial hypertension

被引：4

作者：

Athanasiou, Katherine Alexis ^{[1
,2
]}

Sahni, Sonu ^{[3
,4
]}

Rana, Amrinder ^{[3
,4
]}

Talwar, Arunabh ^{[3
,4
]}

机构：

[1] Arthrit Inst Long Isl, Rheumatol, Hicksville, NY 11801 USA

[2] Northwell Hlth Syst, New Hyde Pk, NY 11040 USA

[3] Dept Pulm Crit Care & Sleep Med, New Hyde Pk, NY USA

[4] Adv Lung Dis Ctr, New Hyde Pk, NY USA

来源：

JAAPA-JOURNAL OF THE AMERICAN ACADEMY OF PHYSICIAN ASSISTANTS | 2017年 / 30卷 / 09期

关键词：

pulmonary arterial hypertension; scleroderma; systemic sclerosis; autoimmune disease; right heart catheterization; vasodilation; RECEPTOR ANTAGONIST BOSENTAN; SYSTEMIC-SCLEROSIS; RISK-FACTORS; DOUBLE-BLIND; DISEASE; ECHOCARDIOGRAPHY; TREPROSTINIL; PREDICTORS; SURVIVAL; EXERCISE;

D O I：

10.1097/01.JAA.0000522129.93995.13

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Scleroderma is an uncommon autoimmune disease of unknown cause that may affect any organ system in the body. Patients with scleroderma are prone to developing pulmonary complications, including pulmonary arterial hypertension (PAH), that are the leading cause of death in this population. This article describes scleroderma-related PAH and its diagnosis and management.

引用

页码：11 / 18

页数：8

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