共 50 条
- [31] Depletion of wild-type huntingtin in mouse models of neurologic diseasesJOURNAL OF NEUROCHEMISTRY, 2003, 87 (01) : 101 - 106Zhang, YU论文数: 0 引用数: 0 h-index: 0机构: Harvard Univ, Sch Med, Brigham & Womens Hosp, Dept Neurosurg,Neuroapoptosis Lab, Boston, MA 02115 USALi, MW论文数: 0 引用数: 0 h-index: 0机构: Harvard Univ, Sch Med, Brigham & Womens Hosp, Dept Neurosurg,Neuroapoptosis Lab, Boston, MA 02115 USADrozda, M论文数: 0 引用数: 0 h-index: 0机构: Harvard Univ, Sch Med, Brigham & Womens Hosp, Dept Neurosurg,Neuroapoptosis Lab, Boston, MA 02115 USAChen, MH论文数: 0 引用数: 0 h-index: 0机构: Harvard Univ, Sch Med, Brigham & Womens Hosp, Dept Neurosurg,Neuroapoptosis Lab, Boston, MA 02115 USARen, SJ论文数: 0 引用数: 0 h-index: 0机构: Harvard Univ, Sch Med, Brigham & Womens Hosp, Dept Neurosurg,Neuroapoptosis Lab, Boston, MA 02115 USASanchez, ROM论文数: 0 引用数: 0 h-index: 0机构: Harvard Univ, Sch Med, Brigham & Womens Hosp, Dept Neurosurg,Neuroapoptosis Lab, Boston, MA 02115 USALeavitt, BR论文数: 0 引用数: 0 h-index: 0机构: Harvard Univ, Sch Med, Brigham & Womens Hosp, Dept Neurosurg,Neuroapoptosis Lab, Boston, MA 02115 USACattaneo, E论文数: 0 引用数: 0 h-index: 0机构: Harvard Univ, Sch Med, Brigham & Womens Hosp, Dept Neurosurg,Neuroapoptosis Lab, Boston, MA 02115 USAFerrante, RJ论文数: 0 引用数: 0 h-index: 0机构: Harvard Univ, Sch Med, Brigham & Womens Hosp, Dept Neurosurg,Neuroapoptosis Lab, Boston, MA 02115 USAHayden, MR论文数: 0 引用数: 0 h-index: 0机构: Harvard Univ, Sch Med, Brigham & Womens Hosp, Dept Neurosurg,Neuroapoptosis Lab, Boston, MA 02115 USAFriedlander, RM论文数: 0 引用数: 0 h-index: 0机构: Harvard Univ, Sch Med, Brigham & Womens Hosp, Dept Neurosurg,Neuroapoptosis Lab, Boston, MA 02115 USA Harvard Univ, Sch Med, Brigham & Womens Hosp, Dept Neurosurg,Neuroapoptosis Lab, Boston, MA 02115 USA
- [32] Expression of wild-type huntingtin in porcine testicular germ cellsJOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY, 2008, 79 : A5 - A5Hruska-Plochan, M.论文数: 0 引用数: 0 h-index: 0机构: Inst Anim Physiol & Genet, Lab Cell Regenerat & Plast, Libechov 27721, Czech Republic Inst Anim Physiol & Genet, Lab Cell Regenerat & Plast, Libechov 27721, Czech RepublicStmadel, J.论文数: 0 引用数: 0 h-index: 0机构: Inst Anim Physiol & Genet, Canc Res Lab, Libechov 27721, Czech Republic Inst Anim Physiol & Genet, Lab Cell Regenerat & Plast, Libechov 27721, Czech RepublicUsvald, D.论文数: 0 引用数: 0 h-index: 0机构: Inst Anim Physiol & Genet, Lab Cell Regenerat & Plast, Libechov 27721, Czech Republic Inst Anim Physiol & Genet, Lab Cell Regenerat & Plast, Libechov 27721, Czech RepublicLackova, M.论文数: 0 引用数: 0 h-index: 0机构: Inst Anim Physiol & Genet, Lab Cell Regenerat & Plast, Libechov 27721, Czech Republic Inst Anim Physiol & Genet, Lab Cell Regenerat & Plast, Libechov 27721, Czech RepublicStruckelova, J.论文数: 0 引用数: 0 h-index: 0机构: Univ Calif San Diego, Dept Anesthesiol, Neuroregenerat Lab, La Jolla, CA 92093 USA Inst Anim Physiol & Genet, Lab Cell Regenerat & Plast, Libechov 27721, Czech RepublicMarsala, M.论文数: 0 引用数: 0 h-index: 0机构: Univ Calif San Diego, Dept Anesthesiol, Neuroregenerat Lab, La Jolla, CA 92093 USA Inst Anim Physiol & Genet, Lab Cell Regenerat & Plast, Libechov 27721, Czech RepublicMotlik, J.论文数: 0 引用数: 0 h-index: 0机构: Inst Anim Physiol & Genet, Lab Cell Regenerat & Plast, Libechov 27721, Czech Republic Inst Anim Physiol & Genet, Lab Cell Regenerat & Plast, Libechov 27721, Czech Republic
- [33] The Latent Stem Cell Population Is Retained in the Hippocampus of Transgenic Huntington's Disease Mice but Not Wild-Type MicePLOS ONE, 2011, 6 (03):Walker, Tara L.论文数: 0 引用数: 0 h-index: 0机构: Univ Queensland, Queensland Brain Inst, Brisbane, Qld, Australia Univ Queensland, Queensland Brain Inst, Brisbane, Qld, AustraliaTurnbull, Geoff W.论文数: 0 引用数: 0 h-index: 0机构: Univ Queensland, Queensland Brain Inst, Brisbane, Qld, Australia Univ Queensland, Queensland Brain Inst, Brisbane, Qld, AustraliaMackay, Eirinn W.论文数: 0 引用数: 0 h-index: 0机构: Univ Queensland, Queensland Brain Inst, Brisbane, Qld, Australia Univ Queensland, Queensland Brain Inst, Brisbane, Qld, AustraliaHannan, Anthony J.论文数: 0 引用数: 0 h-index: 0机构: Univ Melbourne, Howard Florey Inst, Melbourne, Vic 3010, Australia Univ Queensland, Queensland Brain Inst, Brisbane, Qld, AustraliaBartlett, Perry F.论文数: 0 引用数: 0 h-index: 0机构: Univ Queensland, Queensland Brain Inst, Brisbane, Qld, Australia Univ Queensland, Queensland Brain Inst, Brisbane, Qld, Australia
- [34] Huntingtin-lowering strategies for Huntington's diseaseEXPERT OPINION ON INVESTIGATIONAL DRUGS, 2020, 29 (10) : 1125 - 1132Barker, Roger A.论文数: 0 引用数: 0 h-index: 0机构: Univ Cambridge, Dept Clin Neurosci, John Van Geest Ctr Brain Repair, Cambridge CB2 0PY, England Univ Cambridge, MRC WT Cambridge Stem Cell Inst, Cambridge CB2 0PY, England Univ Cambridge, Dept Clin Neurosci, John Van Geest Ctr Brain Repair, Cambridge CB2 0PY, EnglandFujimaki, Motoki论文数: 0 引用数: 0 h-index: 0机构: Cambridge Inst Med Res, Dept Med Genet, Keith Peters Bldg,Cambridge Biomed Campus, Cambridge CB2 0XY, England UK Dementia Res Inst, Cambridge, England Univ Cambridge, Dept Clin Neurosci, John Van Geest Ctr Brain Repair, Cambridge CB2 0PY, EnglandRogers, Priya论文数: 0 引用数: 0 h-index: 0机构: Univ Cambridge, Dept Clin Neurosci, John Van Geest Ctr Brain Repair, Cambridge CB2 0PY, England Univ Cambridge, MRC WT Cambridge Stem Cell Inst, Cambridge CB2 0PY, England Univ Cambridge, Dept Clin Neurosci, John Van Geest Ctr Brain Repair, Cambridge CB2 0PY, EnglandRubinsztein, David C.论文数: 0 引用数: 0 h-index: 0机构: Cambridge Inst Med Res, Dept Med Genet, Keith Peters Bldg,Cambridge Biomed Campus, Cambridge CB2 0XY, England UK Dementia Res Inst, Cambridge, England Univ Cambridge, Dept Clin Neurosci, John Van Geest Ctr Brain Repair, Cambridge CB2 0PY, England
- [35] Huntington's disease: Huntingtin and the control of axonal transportJOURNAL OF NEUROCHEMISTRY, 2009, 110 : 60 - 60Zala, D.论文数: 0 引用数: 0 h-index: 0机构: Inst Curie, CNRS UMR, F-91405 Orsay, France Inst Curie, CNRS UMR, F-91405 Orsay, FranceLiot, G.论文数: 0 引用数: 0 h-index: 0机构: Inst Curie, CNRS UMR, F-91405 Orsay, France Inst Curie, CNRS UMR, F-91405 Orsay, FranceHumbert, S.论文数: 0 引用数: 0 h-index: 0机构: Inst Curie, CNRS UMR, F-91405 Orsay, France Inst Curie, CNRS UMR, F-91405 Orsay, FranceSaudou, F.论文数: 0 引用数: 0 h-index: 0机构: Inst Curie, CNRS UMR, F-91405 Orsay, France Inst Curie, CNRS UMR, F-91405 Orsay, France
- [36] Huntingtin Lowering Strategies for Disease Modification in Huntington's DiseaseNEURON, 2019, 101 (05) : 801 - 819Tabrizi, Sarah J.论文数: 0 引用数: 0 h-index: 0机构: UCL, UCL Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London, England UCL, UK Dementia Res Inst DRI, London, England UCL, UCL Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London, EnglandGhosh, Rhia论文数: 0 引用数: 0 h-index: 0机构: UCL, UCL Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London, England UCL, UCL Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London, EnglandLeavitt, Blair R.论文数: 0 引用数: 0 h-index: 0机构: Univ British Columbia, BC Childrens Hosp, UBC Ctr Huntingtons Dis, Dept Med Genet, Vancouver, BC, Canada Univ British Columbia, BC Childrens Hosp, Ctr Mol Med & Therapeut, Vancouver, BC, Canada UCL, UCL Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London, England
- [37] Targeting Huntingtin Expression in Patients with Huntington's DiseaseNEW ENGLAND JOURNAL OF MEDICINE, 2019, 380 (24): : 2307 - 2316Tabrizi, Sarah J.论文数: 0 引用数: 0 h-index: 0机构: UCL, Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London WC1N 3BG, England UCL, UK Dementia Res Inst, London, England UCL, Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London WC1N 3BG, EnglandLeavitt, Blair R.论文数: 0 引用数: 0 h-index: 0机构: Univ British Columbia, Dept Med Genet, Ctr Huntingtons Dis, Vancouver, BC, Canada Univ British Columbia, Dept Med, Div Neurol, Vancouver, BC, Canada BC Childrens Hosp, Ctr Mol Med & Therapeut, Vancouver, BC, Canada UCL, Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London WC1N 3BG, EnglandLandwehrmeyer, G. Bernhard论文数: 0 引用数: 0 h-index: 0机构: Ulm Univ, Dept Neurol, Huntingtons Dis Ctr, Ulm, Germany UCL, Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London WC1N 3BG, EnglandWild, Edward J.论文数: 0 引用数: 0 h-index: 0机构: UCL, Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London WC1N 3BG, England UCL, UK Dementia Res Inst, London, England UCL, Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London WC1N 3BG, EnglandSaft, Carsten论文数: 0 引用数: 0 h-index: 0机构: Ruhr Univ Bochum, St Josef Hosp, Huntington Ctr North Rhine Westphalia, Dept Neurol, Bochum, Germany UCL, Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London WC1N 3BG, EnglandBarker, Roger A.论文数: 0 引用数: 0 h-index: 0机构: Univ Cambridge, Addenbrookes Hosp, Dept Clin Neurosci, Cambridge, England UCL, Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London WC1N 3BG, EnglandBlair, Nick F.论文数: 0 引用数: 0 h-index: 0机构: Univ Cambridge, Addenbrookes Hosp, Dept Clin Neurosci, Cambridge, England UCL, Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London WC1N 3BG, EnglandCraufurd, David论文数: 0 引用数: 0 h-index: 0机构: Manchester Univ NHS Fdn Trust, St Marys Hosp, Manchester Ctr Genom Med, Manchester, Lancs, England Univ Manchester, Manchester Acad Hlth Sci Ctr, Fac Biol Med & Hlth, Div Evolut & Genom Sci,Sch Biol Sci, Manchester, Lancs, England UCL, Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London WC1N 3BG, England论文数: 引用数: h-index:机构:Rickards, Hugh论文数: 0 引用数: 0 h-index: 0机构: Univ Hosp Birmingham, Inst Clin Sci, Coll Med & Dent Sci, Birmingham, W Midlands, England UCL, Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London WC1N 3BG, EnglandRosser, Anne论文数: 0 引用数: 0 h-index: 0机构: Cardiff Univ, Brain Repair Grp, Brain Repair & Intracranial Neurotherapeut Unit, Neurosci & Mental Hlth Res Inst, Cardiff, S Glam, Wales Sch Biosci, Cardiff, S Glam, Wales UCL, Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London WC1N 3BG, EnglandKordasiewicz, Holly B.论文数: 0 引用数: 0 h-index: 0机构: Ionis Pharmaceut, Carlsbad, CA USA UCL, Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London WC1N 3BG, EnglandCzech, Christian论文数: 0 引用数: 0 h-index: 0机构: F Hoffmann La Roche, Basel, Switzerland UCL, Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London WC1N 3BG, EnglandSwayze, Eric E.论文数: 0 引用数: 0 h-index: 0机构: Ionis Pharmaceut, Carlsbad, CA USA UCL, Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London WC1N 3BG, EnglandNorris, Daniel A.论文数: 0 引用数: 0 h-index: 0机构: Ionis Pharmaceut, Carlsbad, CA USA UCL, Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London WC1N 3BG, EnglandBaumann, Tiffany论文数: 0 引用数: 0 h-index: 0机构: Ionis Pharmaceut, Carlsbad, CA USA UCL, Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London WC1N 3BG, EnglandGerlach, Irene论文数: 0 引用数: 0 h-index: 0机构: F Hoffmann La Roche, Basel, Switzerland UCL, Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London WC1N 3BG, EnglandSchobel, Scott A.论文数: 0 引用数: 0 h-index: 0机构: F Hoffmann La Roche, Basel, Switzerland UCL, Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London WC1N 3BG, EnglandPaz, Erika论文数: 0 引用数: 0 h-index: 0机构: Ionis Pharmaceut, Carlsbad, CA USA UCL, Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London WC1N 3BG, EnglandSmith, Anne V.论文数: 0 引用数: 0 h-index: 0机构: Ionis Pharmaceut, Carlsbad, CA USA UCL, Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London WC1N 3BG, EnglandBennett, C. Frank论文数: 0 引用数: 0 h-index: 0机构: Ionis Pharmaceut, Carlsbad, CA USA UCL, Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London WC1N 3BG, EnglandLane, Roger M.论文数: 0 引用数: 0 h-index: 0机构: Ionis Pharmaceut, Carlsbad, CA USA UCL, Queen Sq Inst Neurol, Dept Neurodegenerat Dis, Huntingtons Dis Ctr, London WC1N 3BG, England
- [38] SUMO modification of Huntingtin and Huntington's disease pathologySCIENCE, 2004, 304 (5667) : 100 - 104Steffan, JS论文数: 0 引用数: 0 h-index: 0机构: Univ Calif Irvine, Dept Dev & Cell Biol, Irvine, CA 92697 USAAgrawal, N论文数: 0 引用数: 0 h-index: 0机构: Univ Calif Irvine, Dept Dev & Cell Biol, Irvine, CA 92697 USAPallos, J论文数: 0 引用数: 0 h-index: 0机构: Univ Calif Irvine, Dept Dev & Cell Biol, Irvine, CA 92697 USARockabrand, E论文数: 0 引用数: 0 h-index: 0机构: Univ Calif Irvine, Dept Dev & Cell Biol, Irvine, CA 92697 USATrotman, LC论文数: 0 引用数: 0 h-index: 0机构: Univ Calif Irvine, Dept Dev & Cell Biol, Irvine, CA 92697 USASlepko, N论文数: 0 引用数: 0 h-index: 0机构: Univ Calif Irvine, Dept Dev & Cell Biol, Irvine, CA 92697 USAIlles, K论文数: 0 引用数: 0 h-index: 0机构: Univ Calif Irvine, Dept Dev & Cell Biol, Irvine, CA 92697 USALukacsovich, T论文数: 0 引用数: 0 h-index: 0机构: Univ Calif Irvine, Dept Dev & Cell Biol, Irvine, CA 92697 USAZhu, YZ论文数: 0 引用数: 0 h-index: 0机构: Univ Calif Irvine, Dept Dev & Cell Biol, Irvine, CA 92697 USACattaneo, E论文数: 0 引用数: 0 h-index: 0机构: Univ Calif Irvine, Dept Dev & Cell Biol, Irvine, CA 92697 USAPandolfi, PP论文数: 0 引用数: 0 h-index: 0机构: Univ Calif Irvine, Dept Dev & Cell Biol, Irvine, CA 92697 USAThompson, LM论文数: 0 引用数: 0 h-index: 0机构: Univ Calif Irvine, Dept Dev & Cell Biol, Irvine, CA 92697 USAMarsh, JL论文数: 0 引用数: 0 h-index: 0机构: Univ Calif Irvine, Dept Dev & Cell Biol, Irvine, CA 92697 USA
- [39] QUANTIFYING MUTANT HUNTINGTIN IN HUNTINGTON'S DISEASE CSFJOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY, 2014, 85 (10):Wild, Edward论文数: 0 引用数: 0 h-index: 0机构: UCL Inst Neurol, London, England UCL Inst Neurol, London, EnglandRobertson, Nicola论文数: 0 引用数: 0 h-index: 0机构: UCL Inst Neurol, London, England UCL Inst Neurol, London, EnglandMiller, James论文数: 0 引用数: 0 h-index: 0机构: UCL Inst Neurol, London, England UCL Inst Neurol, London, EnglandTraeger, Ulrike论文数: 0 引用数: 0 h-index: 0机构: UCL Inst Neurol, London, England UCL Inst Neurol, London, EnglandHaider, Salman论文数: 0 引用数: 0 h-index: 0机构: UCL Inst Neurol, London, England UCL Inst Neurol, London, EnglandMacdonald, Douglas论文数: 0 引用数: 0 h-index: 0机构: CHDI Fdn Inc, London, England UCL Inst Neurol, London, EnglandLangbehn, Douglas论文数: 0 引用数: 0 h-index: 0机构: Univ Iowa, Coll Med, Iowa City, IA USA UCL Inst Neurol, London, EnglandKuhn, Rainer论文数: 0 引用数: 0 h-index: 0机构: IRBM Promidis, Pomezia, Italy UCL Inst Neurol, London, EnglandWeiss, Andreas论文数: 0 引用数: 0 h-index: 0机构: IRBM Promidis, Pomezia, Italy UCL Inst Neurol, London, EnglandTabrizi, Sarah论文数: 0 引用数: 0 h-index: 0机构: UCL Inst Neurol, London, England UCL Inst Neurol, London, England
- [40] Huntingtin Aggregates in the Olfactory Bulb in Huntington's DiseaseFRONTIERS IN AGING NEUROSCIENCE, 2020, 12Highet, Blake论文数: 0 引用数: 0 h-index: 0机构: Univ Auckland, Fac Med & Hlth Sci, Dept Anat & Med Imaging, Auckland, New Zealand Univ Auckland, Fac Med & Hlth Sci, Ctr Brain Res, Auckland, New Zealand Univ Auckland, Fac Med & Hlth Sci, Dept Anat & Med Imaging, Auckland, New Zealand论文数: 引用数: h-index:机构:Murray, Helen C.论文数: 0 引用数: 0 h-index: 0机构: Univ Auckland, Fac Med & Hlth Sci, Dept Anat & Med Imaging, Auckland, New Zealand Univ Auckland, Fac Med & Hlth Sci, Ctr Brain Res, Auckland, New Zealand Univ Auckland, Fac Med & Hlth Sci, Dept Anat & Med Imaging, Auckland, New Zealand论文数: 引用数: h-index:机构:Curtis, Maurice A.论文数: 0 引用数: 0 h-index: 0机构: Univ Auckland, Fac Med & Hlth Sci, Dept Anat & Med Imaging, Auckland, New Zealand Univ Auckland, Fac Med & Hlth Sci, Ctr Brain Res, Auckland, New Zealand Univ Auckland, Fac Med & Hlth Sci, Dept Anat & Med Imaging, Auckland, New Zealand