myositis with anti-mitochondrial antibody type 2;
myositis;
diplopia;
ptosis;
PROGRESSIVE EXTERNAL OPHTHALMOPLEGIA;
PRIMARY BILIARY-CIRRHOSIS;
MITOCHONDRIAL;
AUTOANTIBODIES;
MYOPATHY;
D O I:
10.2169/internalmedicine.7031-21
中图分类号:
R5 [内科学];
学科分类号:
1002 ;
100201 ;
摘要:
Anti-mitochondrial antibody type 2 is a diagnostic marker of primary biliary cirrhosis and complicates myositis. Myositis with anti-mitochondrial antibody type 2 is clinically characterized by slowly progressive limb, cardiac, and respiratory muscle weakness as well as serum creatinine kinase elevations. However, there has been few cases with eye symptoms. We herein report a 59-year-old woman with anti-mitochondrial antibody type 2 who presented with diplopia and ptosis. Magnetic resonance imaging revealed bilateral ocular muscle enlargement and abnormally high intensities in the lower limb muscles. Corticosteroid therapy improved these symptoms. Myositis with anti-mitochondrial antibody type 2 can present with eye symptoms.
机构:
Sakakibara Heart Inst, Dept Cardiol, 3-16-1 Asahi cho, Fuchu, Tokyo 1830003, Japan
Natl Def Med Coll, Dept Cardiol, 3-2 Namiki, Tokorozawa, Saitama 3598513, JapanSakakibara Heart Inst, Dept Cardiol, 3-16-1 Asahi cho, Fuchu, Tokyo 1830003, Japan
Nagatomo, Yuji
Yoshizawa, Saeko
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机构:
Tokyo Womens Med Univ, Dept Surg Pathol, 8-1 Kawada Cho,Shinjuku Ku, Tokyo 1628666, JapanSakakibara Heart Inst, Dept Cardiol, 3-16-1 Asahi cho, Fuchu, Tokyo 1830003, Japan
Yoshizawa, Saeko
Oya, Yasushi
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机构:
Natl Ctr Hosp, Dept Neurol, Natl Ctr Neurol & Psychiat, 4-1-1 Ogawa Higashi, Kodaira, Tokyo 1878551, JapanSakakibara Heart Inst, Dept Cardiol, 3-16-1 Asahi cho, Fuchu, Tokyo 1830003, Japan
机构:
Hakodate Municipal Hosp, Dept Neurol, Hakodate, Hokkaido, JapanHakodate Municipal Hosp, Dept Neurol, Hakodate, Hokkaido, Japan
Fujii, Shintaro
Horiuchi, Kazuhiro
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机构:
Hakodate Municipal Hosp, Dept Neurol, Hakodate, Hokkaido, JapanHakodate Municipal Hosp, Dept Neurol, Hakodate, Hokkaido, Japan
Horiuchi, Kazuhiro
Oshima, Yuki
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机构:
Hakodate Municipal Hosp, Dept Neurol, Hakodate, Hokkaido, JapanHakodate Municipal Hosp, Dept Neurol, Hakodate, Hokkaido, Japan
Oshima, Yuki
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机构:
Eguchi, Katsuki
Nagai, Azusa
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h-index: 0
机构:
Hokkaido Univ, Fac Med, Dept Neurol, Sapporo, Hokkaido, Japan
Hokkaido Univ, Grad Sch Med, Sapporo, Hokkaido, JapanHakodate Municipal Hosp, Dept Neurol, Hakodate, Hokkaido, Japan
Nagai, Azusa
Iwata, Ikuko
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机构:
Hokkaido Univ, Fac Med, Dept Neurol, Sapporo, Hokkaido, Japan
Hokkaido Univ, Grad Sch Med, Sapporo, Hokkaido, JapanHakodate Municipal Hosp, Dept Neurol, Hakodate, Hokkaido, Japan
Iwata, Ikuko
Matsushima, Masaaki
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机构:
Hokkaido Univ, Fac Med, Dept Neurol, Sapporo, Hokkaido, Japan
Hokkaido Univ, Grad Sch Med, Sapporo, Hokkaido, JapanHakodate Municipal Hosp, Dept Neurol, Hakodate, Hokkaido, Japan
Matsushima, Masaaki
Yabe, Ichiro
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h-index: 0
机构:
Hokkaido Univ, Fac Med, Dept Neurol, Sapporo, Hokkaido, Japan
Hokkaido Univ, Grad Sch Med, Sapporo, Hokkaido, JapanHakodate Municipal Hosp, Dept Neurol, Hakodate, Hokkaido, Japan