Structural basis for the enzymatic resistance of the GM2 ganglioside

被引:0
|
作者
Li, YT
Li, SC
Ishida, H
Kiso, M
Raimondi, L
Bernardi, A
Sonnino, S
机构
[1] Tulane Univ, Ctr Hlth Sci, Sch Med & Dent, Dept Biochem, New Orleans, LA 70112 USA
[2] Univ Milan, Dept Organ & Ind Chem, Milan, Italy
关键词
D O I
暂无
中图分类号
Q5 [生物化学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:242 / 264
页数:23
相关论文
共 50 条
  • [21] CHARACTERIZATION OF ANTI-SERUMS FOR GANGLIOSIDE GM2
    SCHWERER, B
    LASSMANN, H
    BERNHEIMER, H
    HOPPE-SEYLERS ZEITSCHRIFT FUR PHYSIOLOGISCHE CHEMIE, 1980, 361 (09): : 1343 - 1343
  • [22] Synthetic studies on sialoglyconjugates .94. Synthesis of 6'-GM2, a regioisomer of ganglioside GM2, for studying the mechanism of action of GM2 activator
    Ishida, H
    Ito, Y
    Tanahashi, E
    Li, YT
    Kiso, M
    Hasegawa, A
    CARBOHYDRATE RESEARCH, 1997, 302 (3-4) : 223 - 227
  • [23] Inefficient conversion of ganglioside GM3 to GM2 by GM2 synthase located in early portions of the secretory pathway
    Allende, ML
    Li, JH
    Darling, DS
    Worth, CA
    Young, WW
    GLYCOBIOLOGY, 1999, 9 (10) : 1137 - 1137
  • [24] Human melanoma GM2 ganglioside is identical to the major ganglioside of salmon liver
    Berard, F
    Terrier, M
    Portoukalian, J
    Thomas, L
    JOURNAL OF INVESTIGATIVE DERMATOLOGY, 1996, 107 (02) : P53 - P53
  • [25] ACCUMULATION OF GANGLIOSIDE GM2 IN CEREBROSPINAL-FLUID OF A PATIENT WITH THE VARIANT AB OF INFANTILE GM2 GANGLIOSIDOSIS
    PULLARKAT, RK
    REHA, H
    BERATIS, NG
    PEDIATRICS, 1981, 68 (01) : 106 - 108
  • [26] CAT WITH HEXOSAMINIDASE DEFICIENCY AND CEREBRAL STORAGE OF GM2 GANGLIOSIDE
    MURPHY, JV
    CORK, LC
    BAKER, HJ
    NEUROLOGY, 1976, 26 (04) : 393 - 393
  • [27] Encephaloneuropathy with lysosomal zebra bodies and GM2 ganglioside storage
    Stromme, P
    Mansson, JE
    Scott, H
    Skullerud, K
    Hovig, T
    PEDIATRIC NEUROLOGY, 1997, 16 (02) : 141 - 144
  • [28] ANTISERA AGAINST GANGLIOSIDE GM2 - IMMUNOCHEMICAL AND IMMUNOHISTOLOGICAL STUDIES
    SCHWERER, B
    LASSMANN, H
    BERNHEIMER, H
    NEUROPATHOLOGY AND APPLIED NEUROBIOLOGY, 1982, 8 (03) : 217 - 226
  • [29] Degradation of membrane-bound ganglioside GM2 by β-hexosaminidase A -: Stimulation by GM2 activator protein and lysosomal lipids
    Werth, N
    Schuette, CG
    Wilkening, G
    Lemm, T
    Sandhoff, K
    JOURNAL OF BIOLOGICAL CHEMISTRY, 2001, 276 (16) : 12685 - 12690
  • [30] Requirement of GM2 ganglioside activator for phospholipase D activation
    Nakamura, S
    Akisue, T
    Jinnai, H
    Hitomi, T
    Sarkar, S
    Miwa, N
    Okada, T
    Yoshida, K
    Kuroda, S
    Kikkawa, U
    Nishizuka, Y
    PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1998, 95 (21) : 12249 - 12253