Severe pyruvate kinase deficiency anemia - A case report

被引：0

作者：

Ghidini, A ^{[1
]}

Korker, VL ^{[1
]}

机构：

[1] Alexandria Hosp, Perinatal Diagnost Ctr, Alexandria, VA USA

来源：

JOURNAL OF REPRODUCTIVE MEDICINE | 1998年 / 43卷 / 08期

关键词：

pyruvate kinase; anemia; pregnancy complications;

D O I：

暂无

中图分类号：

R71 [妇产科学];

学科分类号：

100211 ;

摘要：

BACKGROUND: Pyruvate kinase deficiency is a rare cause of hemolytic anemia and, in its most severe form, requires splenectomy in childhood. During pregnancy, severe cases have been traditionally managed with prophylactic blood transfusions to keep the hemoglobin concentration above arbitrary thresholds of 7-8 g/dL. CASE: A case of severe pyruvate kinase deficiency anemia was managed conservatively without blood transfusions even though the hemoglobin concentration reached a nadir of 6.8 g/dL. The perinatal outcome was good. CONCLUSION: In cases of severe pyruvate kinase deficiency anemia, pregnancy per se might not be an indication for prophylactic blood transfusions.

引用

页码：713 / 715

页数：3

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