Absent pulmonary valve syndrome with ascending aortic aneurysm

被引:4
|
作者
Liang, Chi-Di [1 ]
Ko, Sheung-Fat [2 ]
Chang, Jen-Ping [3 ]
Huang, Shun-Chen [4 ]
机构
[1] Chang Gung Univ, Chang Gung Mem Hosp, Dept Pediat, Kaohsiung Med Ctr,Coll Med, Kaohsiung 833, Taiwan
[2] Chang Gung Univ, Chang Gung Mem Hosp, Dept Radiol, Kaohsiung Med Ctr,Coll Med, Kaohsiung, Taiwan
[3] Chang Gung Univ, Chang Gung Mem Hosp, Dept Cardiovasc Surg, Kaohsiung Med Ctr,Coll Med, Kaohsiung, Taiwan
[4] Chang Gung Univ, Chang Gung Mem Hosp, Dept Anat Pathol, Kaohsiung Med Ctr,Coll Med, Kaohsiung, Taiwan
关键词
Absent pulmonary valve syndrome; Intact ventricular septum; Pulmonary artery; Ascending aorta; Aneurysm; MARFAN PATIENTS; ROOT; ABNORMALITIES; EXPERIENCE; CHILDREN; DISEASE; ARTERY;
D O I
10.1007/s00380-010-0014-3
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Absent pulmonary valve syndrome is rare. We report the case of a child with absent pulmonary valve syndrome noted after birth. Progressive dilatation of the main pulmonary artery and ascending aorta were noted by echocardiography and confirmed by heart computed tomography. He underwent ascending aorta graft replacement and pulmonary artery reduction angioplasty at the age of 6. Good outcome was achieved at 18-month follow-up where subsequent computed tomography revealed a normal size ascending aorta and main pulmonary artery.
引用
收藏
页码:569 / 572
页数:4
相关论文
共 50 条
  • [41] Tetralogy of Fallot With Absent Pulmonary Valve Syndrome, Right Aortic Arch, and Disconnected Left Pulmonary Artery
    Solana-Gracia, Ruth
    Crossland, David
    Mitchell, Leslie
    Wren, Christopher
    Griselli, Massimo
    WORLD JOURNAL FOR PEDIATRIC AND CONGENITAL HEART SURGERY, 2013, 4 (02) : 206 - 209
  • [42] Surgical Management of Absent Pulmonary Valve Syndrome
    Jonas, Richard A.
    WORLD JOURNAL FOR PEDIATRIC AND CONGENITAL HEART SURGERY, 2016, 7 (05) : 600 - 604
  • [43] Prenatal diagnosis of absent pulmonary valve syndrome
    Han, Jiancheng
    He, Yihua
    JOURNAL OF THE AMERICAN COLLEGE OF CARDIOLOGY, 2015, 66 (16) : C258 - C258
  • [44] Absent Pulmonary Valve Syndrome with Left Hemitruncus
    Aly, Ashraf M.
    Reid, Deborah A.
    Jiwani, Amyn K.
    Desai, Pooja H.
    AJP REPORTS, 2012, 2 (01): : 51 - 53
  • [45] TETRALOGY OF FALLOT WITH ABSENT PULMONARY VALVE SYNDROME
    Dossey, A. M.
    Imamura, M.
    Richter, G.
    JOURNAL OF INVESTIGATIVE MEDICINE, 2011, 59 (02) : 441 - 441
  • [46] ABSENT PULMONARY VALVE SYNDROME - CONSIDERATIONS OF MANAGEMENT
    PINSKY, WW
    NIHILL, MR
    MULLINS, CE
    HARRISON, G
    MCNAMARA, DG
    CIRCULATION, 1978, 57 (01) : 159 - 162
  • [47] Prenatal diagnosis of absent pulmonary valve syndrome
    Moleiro, Maria Lucia
    Guedes-Martins, Luis
    BMJ CASE REPORTS, 2021, 14 (01)
  • [48] Approach to the patient with biscuspid aortic valve and ascending aorta aneurysm
    Ortiz J.T.
    Shin D.D.
    Rajamannan N.M.
    Current Treatment Options in Cardiovascular Medicine, 2006, 8 (6) : 461 - 467
  • [49] TREATMENT OF ABSENT PULMONARY VALVE SYNDROME WITH HOMOGRAFT
    KRON, IL
    JOHNSON, AM
    CARPENTER, MA
    GUTGESELL, HP
    OVERHOLT, ED
    RHEUBAN, KS
    ANNALS OF THORACIC SURGERY, 1988, 46 (05): : 579 - 581
  • [50] A saccular aneurysm on the ascending aorta following aortic valve replacement
    Erdöl, C
    Çelik, S
    Baykan, M
    INTERNATIONAL JOURNAL OF CARDIOLOGY, 2001, 79 (2-3) : 263 - 264