Kaposiform lymphangiomatosis in adult patients- results of sirolimus treatment

被引：1
|
作者：
Radzikowska, Elzbieta [1 ]
Blasinska, Katarzyna [1 ]
Szolkowska, Malgorzata [1 ]
Wiatr, Elzbieta [1 ]
机构：
[1] Natl TB & Lung Dis Res Inst, Warsaw, Poland
来源：
EUROPEAN RESPIRATORY JOURNAL | 2021年 / 58卷
关键词：
Treatments; Personalised medicine; Orphan diseases;
D O I：
10.1183/13993003.congress-2021.PA3292
中图分类号：
R56 [呼吸系及胸部疾病];
学科分类号：
摘要：
PA3292
引用
收藏
页数：2
相关论文
共 50 条
  • [21] KAPOSIFORM LYMPHANGIOMATOSIS: CLINICAL FEATURES OF 23 PATIENTS WITH A DISTINCT, AGGRESSIVE LYMPHATIC DISORDER
    Croteau, Stacy
    Kozakewich, Harry
    Perez-Atayde, Antonio
    Chaudry, Gulraiz
    Fishman, Steven
    Mulliken, John
    Trenor, Cameron
    PEDIATRIC BLOOD & CANCER, 2013, 60 : S33 - S33
  • [22] Kaposiform hemangioendothelioma with distant lymphangiomatosis without an association to Kasabach-Merritt-Syndrome in a female adult!
    Vetter-Kauczok, Claudia S.
    Strobel, Philipp
    Brocker, Eva B.
    Becker, Jurgen C.
    VASCULAR HEALTH AND RISK MANAGEMENT, 2008, 4 (01) : 263 - 266
  • [23] SIROLIMUS: ITS ROLE IN THE TREATMENT OF GENERALIZED LYMPHANGIOMATOSIS IN AN ADOLESCENT MALE
    Garcia-Canet, C. E.
    Narsinghani, U.
    JOURNAL OF INVESTIGATIVE MEDICINE, 2019, 67 (02) : 483 - 484
  • [24] Sirolimus for the treatment of progressive kaposiform hemangioendothelioma: A multicenter retrospective study
    Ji, Yi
    Chen, Siyuan
    Xiang, Bo
    Li, Kai
    Xu, Zhicheng
    Yao, Wei
    Lu, Guoyan
    Liu, Xingtao
    Xia, Chuncao
    Wang, Qi
    Li, Yanan
    Wang, Chuan
    Yang, Kaiying
    Yang, Gang
    Tang, Xueyang
    Xu, Ting
    Wu, Hao
    INTERNATIONAL JOURNAL OF CANCER, 2017, 141 (04) : 848 - 855
  • [25] Sirolimus (Rapamycin) in patients with Kaposiform hemangioendothelioma. Clinical case
    Rodriguez Z, Natalie
    Benavides J, Pablo
    REVISTA CHILENA DE PEDIATRIA-CHILE, 2013, 84 (05): : 537 - 544
  • [26] A Phase 2 Clinical Trial Assessing Efficacy And Safety Of The Mtor Inhibitor Sirolimus In The Treatment Of Generalized Lymphatic Anomaly, Kaposiform Lymphangiomatosis, And Gorham-Stout Disease
    Ricci, K. W.
    Trenor, C. C., III
    Hammill, A. M.
    Vinks, A. A.
    Patel, M. N.
    Chaudry, G.
    Wentzel, M. S.
    Mobberley-Schuman, P. S.
    Chute, C.
    Eile, J.
    Gupta, A.
    Merrow, A. C.
    Dasgupta, R.
    Dickie, B. H.
    Azizkhan, R. G.
    Fei, L.
    Hornung, L.
    Adams, D. M.
    AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2015, 191
  • [27] Insights Image for “Treatment of severe Kaposiform Lymphangiomatosis positive for NRAS mutation by MEK-inhibition”
    Guy Chowers
    Gadi Abebe-Campino
    Hana Golan
    Asaf Vivante
    Shoshana Greenberger
    Michalle Soudack
    Galia Barkai
    Ilana Fox-Fisher
    Dong Li
    Michael March
    Mark R. Battig
    Hakon Hakonarson
    Denise Adams
    Yoav Dori
    Adi Dagan
    Pediatric Research, 2023, 94 : 2117 - 2117
  • [28] Additive value of transarterial embolization to systemic sirolimus treatment in kaposiform hemangioendothelioma
    Brill, Richard
    Uller, Wibke
    Huf, Veronika
    Mueller-Wille, Rene
    Schmid, Irene
    Pohl, Alexandra
    Haeberle, Beate
    Perkowski, Sybille
    Funke, Katrin
    Till, Anne-Marie
    Lauten, Melchior
    Neumann, Jacob
    Guettel, Christian
    Heid, Esther
    Ziermann, Franziska
    Schmid, Axel
    Huesemann, Dieter
    Meyer, Lutz
    Sporns, Peter B.
    Schinner, Regina
    Schmidt, Vanessa F.
    Ricke, Jens
    Roessler, Jochen
    Kapp, Friedrich G.
    Wohlgemuth, Walter A.
    Wildgruber, Moritz
    INTERNATIONAL JOURNAL OF CANCER, 2021, 148 (09) : 2345 - 2351
  • [29] Kaposiform hemangioendothelioma with Kasabach-Merritt syndrome: successful treatment with sirolimus
    Reichel, Alexandra
    Hamm, Henning
    Wiegering, Verena
    Wiewrodt, Barbara
    Neubauer, Henning
    Ernestus, Karen
    Winkler, Beate
    JOURNAL DER DEUTSCHEN DERMATOLOGISCHEN GESELLSCHAFT, 2017, 15 (03): : 329 - 331
  • [30] SIROLIMUS FOR THE TREATMENT OF COMPLICATED KAPOSIFORM HEMANGIOENDOTHELIOMAS - PHASE II STUDY UPDATE
    Hammill, Adrienne
    Trenor, Cameron
    Wentzel, Mary Sue
    Chute, Carol
    Merrow, Arnold
    Patel, Manish
    Azizkhan, Richard
    Adams, Denise M.
    PEDIATRIC BLOOD & CANCER, 2013, 60 : S32 - S33
12345