Hugh-Stovin syndrome: the 'incomplete Behcet's disease'. A case study of a young adult with recurrent pulmonary embolism and pulmonary arterial aneurysms

被引：1

作者：

Ukemenam, Chinedu ^{[1
]}

Muppaneni, Sivaram Prabhuji ^{[1
]}

De, Debapriya ^{[1
]}

Lacasse, Alexandre ^{[1
]}

机构：

[1] SSM St Marys Hosp, Dept Internal Med, St Louis, MO 63117 USA

来源：

JOURNAL OF COMMUNITY HOSPITAL INTERNAL MEDICINE PERSPECTIVES | 2021年 / 11卷 / 04期

关键词：

Hugh-Stovin; thrombophlebitis; pulmonary artery aneurysms; vasculitides; Behcet's disease; NOSOLOGY;

D O I：

10.1080/20009666.2020.1816273

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Hugh-Stovin Syndrome (HSS) is characterized by recurrent thrombophlebitis and multiple pulmonary and/or bronchial artery aneurysms indistinguishable from the cardiovascular features seen in Behcet's disease (BD). Our case describes a 30-year-old male with recurrent pulmonary embolism and bilateral pulmonary aneurysms. Autoimmune, hypercoagulable, and infectious work up were negative. Elevated inflammatory markers and absence of the typical clinical findings seen in BD led to the diagnosis of Hugh-Stovin syndrome (HSS). Immunosuppression using steroids and azathioprine led to clinical response. Anticoagulation was continued based on risk/benefit ratio.

引用

页码：566 / 567

页数：2

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